Acute respiratory failure due to cutis laxa pulmonary emphysema treated with high-flow nasal cannula

被引：0

作者：

Perazzo, Tommaso ^{[1
,2
]}

Perazzo, Alessandro ^{[1
]}

Ferraioli, Gianluca ^{[1
]}

Diaz De Teran, Teresa ^{[3
]}

Gonzales, Monica ^{[3
]}

Banfi, Paolo ^{[4
]}

Nicolini, Antonello ^{[1
,4
,5
]}

机构：

[1] Gen Hosp, Resp Dis Unit, Genoa, Italy

[2] Resp Dis & Allergy Clin, Genoa, Italy

[3] Hosp Univ Marques Valdecilla, Div Pulmonol, Santander, Spain

[4] IRCCS Don Gnocchi Fdn, Rehabil Pulmonol, Milan, Italy

[5] Resp Dis Unit, Via Terzi 43, I-16039 Sestri Levante, GE, Italy

来源：

MINERVA RESPIRATORY MEDICINE | 2023年 / 62卷 / 01期

关键词：

Pulmonary emphysema; Cutis laxa; Respiratory insufficiency; Cannula; DOMINANT; ELASTIN; MUTATION; DISEASE;

D O I：

10.23736/S2784-8477.22.01997-0

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

Cutis laxa is a rare connective tissue disorder characterized by progressive loosening of the skin, associated with abnor-malities of other organs such as the lung. We present a case of this disease with pulmonary emphysema and acute respira-tory failure successfully treated with high-flow nasal cannula.

引用

页码：50 / 53

页数：4

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