Systemic sclerosis

被引：0
|
作者：
Faber, A. -M. [1 ]
Krieg, T. [2 ]
Hunzelmann, N. [1 ]
机构：
[1] Univ Cologne, Klin & Poliklin Dermatol & Venerol, Kerpener Str 62, D-50937 Cologne, Germany
[2] Univ Cologne, Translat Matrix Biol, Med Fak, Cologne, Germany
来源：
DERMATOLOGIE | 2024年 / 75卷 / 03期
基金：
英国科研创新办公室;
关键词：
Quality of life; Scleroderma; Organ-specific treatment; Connective tissue hyperplasia; Interdisciplinary health team; STEM-CELL TRANSPLANTATION; LONG-TERM SURVIVAL; DIGITAL ULCERS; GERMAN NETWORK; SCLERODERMA; CLASSIFICATION; PATHOGENESIS; EPIDEMIOLOGY; INVOLVEMENT; DIAGNOSIS;
D O I：
10.1007/s00105-024-05298-8
中图分类号：
R75 [皮肤病学与性病学];
学科分类号：
100206 ;
摘要：
Background: Systemic sclerosis (SSc) is a very heterogeneous, chronic, rare, but socioeconomically important disease with a severe disease course and severe impairment of the quality of life of affected patients. Objectives: Overview of the current state of research on the pathogenesis, diagnosis and therapy of SSc. Methods: A literature search was performed. Results: The pathogenesis of SSc is not fully understood. ACR/EULAR criteria allow the diagnosis of early forms of SSc. Classification into limited cutaneous SSc and diffuse cutaneous SSc is of prognostic and therapeutic relevance. New organ-specific treatment options for SSc have led to improved quality of life and prognosis.
引用
收藏
页码：181 / 196
页数：16
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