ADAMTS13 conformation is closed in non-immune acquired thrombotic thrombocytopenic purpura of unidentified pathophysiology

被引:12
作者
Joly, Berangere S. [1 ,2 ]
Roose, Elien [3 ]
Coppo, Paul [4 ,5 ]
Vanhoorelbeke, Karen [3 ]
Veyradier, Agnes [1 ,2 ]
机构
[1] Univ Paris, Serv Hematol Biol, Hop Lariboisiere, AP HP Nord, Paris, France
[2] Univ Paris, Inst Univ Hematol, Hop St Louis, EA3518, Paris, France
[3] Katholieke Univ Leuven, Lab Thrombosis Res, IRF Life Sci, Campus Kulak Kortrijk, Kortrijk, Belgium
[4] Hop St Antoine, AP HP, Dept Hematol Clin, Paris, France
[5] Univ Paris 06, Paris, France
基金
欧盟地平线“2020”;
关键词
FACTOR-CLEAVING PROTEASE; ACTIVATION; ANTIBODIES;
D O I
10.3324/haematol.2022.280768
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:638 / 644
页数:7
相关论文
共 16 条
[11]   Open ADAMTS13, induced by antibodies, is a biomarker for subclinical immune-mediated thrombotic thrombocytopenic purpura [J].
Roose, Elien ;
Tellier, An-Sofie ;
Tellier, Edwige ;
Sinkovits, Gyorgy ;
Joly, Berangere S. ;
Dekimpe, Charlotte ;
Kaplanski, Gilles ;
Le Besnerais, Maelle ;
Mancini, Ilaria ;
Falter, Tanja ;
Von Auer, Charis ;
Feys, Hendrik B. ;
Reti, Marienn ;
Rossmann, Heidi ;
Vandenbulcke, Aline ;
Pareyn, Inge ;
Voorberg, Jan ;
Greinacher, Andreas ;
Benhamou, Ygal ;
Deckmyn, Hans ;
Fijnheer, Rob ;
Prohaszka, Zoltan ;
Peyvandi, Flora ;
Lammle, Bernhard ;
Coppo, Paul ;
De Meyer, Simon F. ;
Veyradier, Agnes ;
Vanhoorelbeke, Karen .
BLOOD, 2020, 136 (03) :353-361
[12]   Conformational activation of ADAMTS13 [J].
South, Kieron ;
Luken, Brenda M. ;
Crawley, James T. B. ;
Phillips, Rebecca ;
Thomas, Mari ;
Collins, Richard F. ;
Deforche, Louis ;
Vanhoorelbeke, Karen ;
Lane, David A. .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2014, 111 (52) :18578-18583
[13]   Thrombotic Thrombocytopenic Purpura: Pathophysiology, Diagnosis, and Management [J].
Sukumar, Senthil ;
Lammle, Bernhard ;
Cataland, Spero R. .
JOURNAL OF CLINICAL MEDICINE, 2021, 10 (03) :1-24
[14]   Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura [J].
Tsai, HM ;
Lian, ECY .
NEW ENGLAND JOURNAL OF MEDICINE, 1998, 339 (22) :1585-1594
[15]  
Waele LD, 2021, BLOOD ADV, V5, P4480
[16]   Structure of von Willebrand factor-cleaving protease (ADAMTS13), a metalloprotease involved in thrombotic thrombocytopenic purpura [J].
Zheng, XL ;
Chung, D ;
Takayama, TK ;
Majerus, EM ;
Sadler, JE ;
Fujikawa, K .
JOURNAL OF BIOLOGICAL CHEMISTRY, 2001, 276 (44) :41059-41063