Autoimmune pancreatitis (AIP) is a fibro-inflammatory disease characterized by inflammation and fibrosis of the pancreas. It is a systemic disease that can affect multiple organs, including the bile ducts, kidneys, lungs, and other organs. However, due to its complex presentation, AIP is often challenging to diagnose, and misdiagnosis with pancreatic tumors can occur. In our study, we reviewed three cases of atypical AIP where patients had normal serum IgG4 levels, leading to initial misdiagnosis with pancreatic tumors. Delayed diagnosis resulted in irreversible pathologies such as retroperitoneal fibrosis. All three patients had bile duct involvement, and imaging findings were similar to those of tumors, further complicating the diagnosis. The correct diagnosis was confirmed only after diagnostic therapy. Our study aims to raise awareness of atypical AIP and improve diagnostic efficiency by analyzing the clinical characteristics of these patients.
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Yokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Kubota, Kensuke
Iida, Hiroshi
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Yokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Iida, Hiroshi
Fujisawa, Toshio
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Yokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Fujisawa, Toshio
Yoneda, Masato
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Yokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Yoneda, Masato
Inamori, Masahiko
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Yokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Inamori, Masahiko
Abe, Yasunobu
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Yokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Abe, Yasunobu
Kirikoshi, Hiroyuki
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Yokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Kirikoshi, Hiroyuki
Saito, Satoru
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Yokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Saito, Satoru
Ohshiro, Hisashi
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Yokohama City Univ, Grad Sch Med, Div Pathol, Yokohama, Kanagawa 232, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Ohshiro, Hisashi
Kakuta, Yukio
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Yokohama Rosai Hosp, Div Pathol, Yokohama, Kanagawa, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
Kakuta, Yukio
Nakajima, Atushi
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Yokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, JapanYokohama City Univ, Div Gastroenterol, Grad Sch Med, Kanazawa Ku, Yokohama, Kanagawa 2360004, Japan
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Shanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R ChinaShanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R China
Li, Gaopeng
Liu, Ting
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Shanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R ChinaShanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R China
Liu, Ting
Zheng, Jian
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Shanxi Med Univ, Dept Crit Care Med, Hosp Shanxi Univ Tradit Chinese Med, Hosp 1, Taiyuan, Shanxi, Peoples R ChinaShanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R China
Zheng, Jian
Kang, Wenqin
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Hosp Shanxi Univ Tradit Chinese Med, Dept Gen Surg, Taiyuan, Shanxi, Peoples R ChinaShanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R China
Kang, Wenqin
Xu, Jun
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Shanxi Acad Med Sci, Dept Gen Surg, Shanxi Dayi Hosp, Taiyuan, Shanxi, Peoples R ChinaShanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R China
Xu, Jun
Gao, Zefeng
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Shanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R ChinaShanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R China
Gao, Zefeng
Ma, Jinfeng
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Shanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R ChinaShanxi Med Univ, Shanxi Canc Hosp, Dept Gen Surg, Taiyuan, Shanxi, Peoples R China
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Department of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686Department of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Hayashi M.
Arisaka Y.
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Department of Internal Medicine, Osaka Medical College Hospital, Takatsuki CityDepartment of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Arisaka Y.
Takeshita A.
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Department of Pathology, Osaka Medical College Hospital, Takatsuki CityDepartment of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Takeshita A.
Tominaga Y.
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Department of Internal Medicine, Osaka Medical College Hospital, Takatsuki CityDepartment of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Tominaga Y.
Ki T.
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Department of Internal Medicine, Osaka Medical College Hospital, Takatsuki CityDepartment of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Ki T.
Masuda D.
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Department of Internal Medicine, Osaka Medical College Hospital, Takatsuki CityDepartment of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Masuda D.
Hirokawa F.
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Department of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686Department of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Hirokawa F.
Egashira Y.
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机构:
Department of Pathology, Osaka Medical College Hospital, Takatsuki CityDepartment of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Egashira Y.
Tsuji M.
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Department of Pathology, Osaka Medical College Hospital, Takatsuki CityDepartment of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Tsuji M.
Yamamoto K.
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Department of Radiology, Osaka Medical College Hospital, Takatsuki CityDepartment of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Yamamoto K.
Higuchi K.
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Department of Internal Medicine, Osaka Medical College Hospital, Takatsuki CityDepartment of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686
Higuchi K.
Tanigawa N.
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Department of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686Department of General and Gastroenterological Surgery, Osaka Medical College Hospital, Takatsuki City, Osaka 569-8686