共 6 条
[1]
Dysfunctional Inflammation in Cystic Fibrosis Airways: From Mechanisms to Novel Therapeutic Approaches
[J].
Ghigo, Alessandra
;
Prono, Giulia
;
Riccardi, Elisa
;
De Rose, Virginia
.
INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES,
2021, 22 (04)
:1-23

Ghigo, Alessandra
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Torino, Dept Mol Biotechnol & Hlth Sci, Ctr Mol Biotechnol, I-10126 Turin, Italy Univ Torino, Dept Mol Biotechnol & Hlth Sci, Ctr Mol Biotechnol, I-10126 Turin, Italy

Prono, Giulia
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Torino, Dept Mol Biotechnol & Hlth Sci, Ctr Mol Biotechnol, I-10126 Turin, Italy Univ Torino, Dept Mol Biotechnol & Hlth Sci, Ctr Mol Biotechnol, I-10126 Turin, Italy

Riccardi, Elisa
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Torino, Postgrad Sch Resp Med, I-10126 Turin, Italy Univ Torino, Dept Mol Biotechnol & Hlth Sci, Ctr Mol Biotechnol, I-10126 Turin, Italy

De Rose, Virginia
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Torino, Dept Mol Biotechnol & Hlth Sci, Ctr Mol Biotechnol, I-10126 Turin, Italy Univ Torino, Dept Mol Biotechnol & Hlth Sci, Ctr Mol Biotechnol, I-10126 Turin, Italy
[2]
Ivacaftor and Airway Inflammation in Preschool Children with Cystic Fibrosis
[J].
McNally, Paul
;
Butler, Daryl
;
Karpievitch, Yuliya V.
;
Linnane, Barry
;
Ranganathan, Sarath
;
Stick, Stephen M.
;
Hall, Graham L.
;
Schultz, Andre
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
2021, 204 (05)
:605-608

McNally, Paul
论文数: 0 引用数: 0
h-index: 0
机构:
Childrens Hlth Ireland, Dublin, Ireland
Ireland Univ Med & Hlth Sci, Royal Coll Surg, Dublin, Ireland Childrens Hlth Ireland, Dublin, Ireland

Butler, Daryl
论文数: 0 引用数: 0
h-index: 0
机构:
Childrens Hlth Ireland, Dublin, Ireland
Ireland Univ Med & Hlth Sci, Royal Coll Surg, Dublin, Ireland Childrens Hlth Ireland, Dublin, Ireland

Karpievitch, Yuliya V.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Western Australia, Perth, WA, Australia
Telethon Kids Inst, Perth, WA, Australia Childrens Hlth Ireland, Dublin, Ireland

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论文数: 引用数:
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Stick, Stephen M.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Western Australia, Perth, WA, Australia
Telethon Kids Inst, Perth, WA, Australia
Perth Childrens Hosp, Nedlands, WA, Australia Childrens Hlth Ireland, Dublin, Ireland

Hall, Graham L.
论文数: 0 引用数: 0
h-index: 0
机构:
Telethon Kids Inst, Perth, WA, Australia
Curtin Univ, Bentley, WA, Australia Childrens Hlth Ireland, Dublin, Ireland

Schultz, Andre
论文数: 0 引用数: 0
h-index: 0
机构: Childrens Hlth Ireland, Dublin, Ireland
[3]
Clinical Effectiveness of Elexacaftor/Tezacaftor/Ivacaftor in People with Cystic Fibrosis
[J].
Nichols, David P.
;
Paynter, Alex C.
;
Heltshe, Sonya L.
;
Donaldson, Scott H.
;
Frederick, Carla A.
;
Freedman, Steven D.
;
Gelfond, Daniel
;
Hoffman, Lucas R.
;
Kelly, Andrea
;
Narkewicz, Michael R.
;
Pittman, Jessica E.
;
Ratjen, Felix
;
Rosenfeld, Margaret
;
Sagel, Scott D.
;
Schwarzenberg, Sarah Jane
;
Singh, Pradeep K.
;
Solomon, George M.
;
Stalvey, Michael S.
;
Clancy, John P.
;
Kirby, Shannon
;
Van Dalfsen, Jill M.
;
Kloster, Margaret H.
;
Rowe, Steven M.
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
2022, 205 (05)
:529-539

Nichols, David P.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA
Seattle Childrens Res Inst, Cyst Fibrosis Fdn, Therapeut Dev Network Coordinating Ctr, Seattle, WA USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Paynter, Alex C.
论文数: 0 引用数: 0
h-index: 0
机构:
Seattle Childrens Res Inst, Cyst Fibrosis Fdn, Therapeut Dev Network Coordinating Ctr, Seattle, WA USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Heltshe, Sonya L.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA
Seattle Childrens Res Inst, Cyst Fibrosis Fdn, Therapeut Dev Network Coordinating Ctr, Seattle, WA USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Donaldson, Scott H.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ North Carolina, Dept Med, Chapel Hill, NC 27515 USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Frederick, Carla A.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Buffalo, Jacobs Sch Med & Biomed Sci, Buffalo, NY USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Freedman, Steven D.
论文数: 0 引用数: 0
h-index: 0
机构:
Harvard Med Sch, Beth Israel Deaconess Med Ctr, Boston, MA 02115 USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Gelfond, Daniel
论文数: 0 引用数: 0
h-index: 0
机构:
Western New York Pediat Gastroenterol, Buffalo, NY USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Hoffman, Lucas R.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA
Univ Washington, Sch Med, Dept Microbiol, Seattle, WA 98195 USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Kelly, Andrea
论文数: 0 引用数: 0
h-index: 0
机构:
Childrens Hosp Philadelphia, Div Endocrinol & Diabet, Philadelphia, PA 19104 USA
Univ Penn, Dept Pediat, Perelman Sch Med, Philadelphia, PA 19104 USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Narkewicz, Michael R.
论文数: 0 引用数: 0
h-index: 0
机构:
Childrens Hosp Colorado, Digest Hlth Inst, Aurora, CO USA
Univ Colorado, Sch Med, Dept Pediat, Aurora, CO USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Pittman, Jessica E.
论文数: 0 引用数: 0
h-index: 0
机构:
Washington Univ, Sch Med, Dept Pediat, St Louis, MO 63110 USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Ratjen, Felix
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Toronto, Hosp Sick Children, Dept Pediat, Div Resp Med,Translat Med, Toronto, ON, Canada Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

论文数: 引用数:
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Sagel, Scott D.
论文数: 0 引用数: 0
h-index: 0
机构:
Childrens Hosp Colorado, Dept Pediat, Aurora, CO USA
Univ Colorado, Sch Med, Aurora, CO USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Schwarzenberg, Sarah Jane
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Minnesota, Dept Pediat, Mason Childrens Hosp, Minneapolis, MN 55455 USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Singh, Pradeep K.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Washington, Sch Med, Dept Microbiol, Seattle, WA 98195 USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Solomon, George M.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Alabama Birmingham, Dept Med, Birmingham, AL 35294 USA
Univ Alabama Birmingham, Gregory Fleming James Cyst Fibrosis Res Ctr, Birmingham, AL USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Stalvey, Michael S.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Alabama Birmingham, Gregory Fleming James Cyst Fibrosis Res Ctr, Birmingham, AL USA
Dept Pediat, Bethesda, MD USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Clancy, John P.
论文数: 0 引用数: 0
h-index: 0
机构:
Cyst Fibrosis Fdn, Bethesda, MD USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Kirby, Shannon
论文数: 0 引用数: 0
h-index: 0
机构:
Seattle Childrens Res Inst, Cyst Fibrosis Fdn, Therapeut Dev Network Coordinating Ctr, Seattle, WA USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Van Dalfsen, Jill M.
论文数: 0 引用数: 0
h-index: 0
机构:
Seattle Childrens Res Inst, Cyst Fibrosis Fdn, Therapeut Dev Network Coordinating Ctr, Seattle, WA USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Kloster, Margaret H.
论文数: 0 引用数: 0
h-index: 0
机构:
Seattle Childrens Res Inst, Cyst Fibrosis Fdn, Therapeut Dev Network Coordinating Ctr, Seattle, WA USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA

Rowe, Steven M.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Alabama Birmingham, Dept Med, Birmingham, AL 35294 USA
Univ Alabama Birmingham, Gregory Fleming James Cyst Fibrosis Res Ctr, Birmingham, AL USA
Dept Pediat, Bethesda, MD USA Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA
[4]
Inflammation in cystic fibrosis: An update
[J].
Roesch, Erica A.
;
Nichols, David P.
;
Chmiel, James F.
.
PEDIATRIC PULMONOLOGY,
2018, 53
:S30-S50

Roesch, Erica A.
论文数: 0 引用数: 0
h-index: 0
机构: Department of Pediatrics, Case Western Reserve University School of Medicine, Rainbow Babies and Children's Hospital, Cleveland, OH

Nichols, David P.
论文数: 0 引用数: 0
h-index: 0
机构: Department of Pediatrics, Case Western Reserve University School of Medicine, Rainbow Babies and Children's Hospital, Cleveland, OH

Chmiel, James F.
论文数: 0 引用数: 0
h-index: 0
机构: Department of Pediatrics, Case Western Reserve University School of Medicine, Rainbow Babies and Children's Hospital, Cleveland, OH
[5]
Clinical Mechanism of the Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor in G551D-mediated Cystic Fibrosis
[J].
Rowe, Steven M.
;
Heltshe, Sonya L.
;
Gonska, Tanja
;
Donaldson, Scott H.
;
Borowitz, Drucy
;
Gelfond, Daniel
;
Sagel, Scott D.
;
Khan, Umer
;
Mayer-Hamblett, Nicole
;
Van Dalfsen, Jill M.
;
Joseloff, Elizabeth
;
Ramsey, Bonnie W.
.
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE,
2014, 190 (02)
:175-184

Rowe, Steven M.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Heltshe, Sonya L.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA
Cyst Fibrosis Fdn Therapeut Dev Network, Seattle Childrens Res Inst, Seattle, WA USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Gonska, Tanja
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Toronto, Hosp Sick Children, Res Inst, Dept Pediat, Toronto, ON M5G 1X8, Canada Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Donaldson, Scott H.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ N Carolina, Dept Med, Chapel Hill, NC USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Borowitz, Drucy
论文数: 0 引用数: 0
h-index: 0
机构:
SUNY Buffalo, Sch Med & Biomed Sci, Dept Pediat, Buffalo, NY 14260 USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Gelfond, Daniel
论文数: 0 引用数: 0
h-index: 0
机构:
SUNY Buffalo, Sch Med & Biomed Sci, Dept Pediat, Buffalo, NY 14260 USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Sagel, Scott D.
论文数: 0 引用数: 0
h-index: 0
机构:
Childrens Hosp Colorado, Aurora, CO USA
Univ Colorado, Sch Med, Aurora, CO USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Khan, Umer
论文数: 0 引用数: 0
h-index: 0
机构:
Cyst Fibrosis Fdn Therapeut Dev Network, Seattle Childrens Res Inst, Seattle, WA USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Mayer-Hamblett, Nicole
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA
Cyst Fibrosis Fdn Therapeut Dev Network, Seattle Childrens Res Inst, Seattle, WA USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Van Dalfsen, Jill M.
论文数: 0 引用数: 0
h-index: 0
机构:
Cyst Fibrosis Fdn Therapeut Dev Network, Seattle Childrens Res Inst, Seattle, WA USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Joseloff, Elizabeth
论文数: 0 引用数: 0
h-index: 0
机构:
Cyst Fibrosis Fdn Therapeut, Bethesda, MD USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA

Ramsey, Bonnie W.
论文数: 0 引用数: 0
h-index: 0
机构:
Univ Washington, Sch Med, Dept Pediat, Seattle, WA 98195 USA
Cyst Fibrosis Fdn Therapeut Dev Network, Seattle Childrens Res Inst, Seattle, WA USA Univ Alabama, Dept Med, Tuscaloosa, AL 35487 USA
[6]
CFTR Correctors and Antioxidants Partially Normalize Lipid Imbalance but not Abnormal Basal Inflammatory Cytokine Profile in CF Bronchial Epithelial Cells
[J].
Veltman, Mieke
;
De Sanctis, Juan B.
;
Stolarczyk, Marta
;
Klymiuk, Nikolai
;
Baehr, Andrea
;
Brouwer, Rutger W.
;
Oole, Edwin
;
Shah, Juhi
;
Ozdian, Tomas
;
Liao, Jie
;
Martini, Carolina
;
Radzioch, Danuta
;
Hanrahan, John W.
;
Scholte, Bob J.
.
FRONTIERS IN PHYSIOLOGY,
2021, 12

Veltman, Mieke
论文数: 0 引用数: 0
h-index: 0
机构:
Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands
Erasmus MC, Sophia Childrens Hosp, Pediat Pulmonol, Rotterdam, Netherlands Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

De Sanctis, Juan B.
论文数: 0 引用数: 0
h-index: 0
机构:
Palacky Univ, Fac Med & Dent, Inst Mol & Translat Med, Olomouc, Czech Republic Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Stolarczyk, Marta
论文数: 0 引用数: 0
h-index: 0
机构:
Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Klymiuk, Nikolai
论文数: 0 引用数: 0
h-index: 0
机构:
Tech Univ Munich, Large Anim Models Cardiovasc Res, Munich, Germany
Ludwig Maximilians Univ Munchen, Ctr Innovat Med Models, Munich, Germany Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Baehr, Andrea
论文数: 0 引用数: 0
h-index: 0
机构:
Tech Univ Munich, Large Anim Models Cardiovasc Res, Munich, Germany
Ludwig Maximilians Univ Munchen, Ctr Innovat Med Models, Munich, Germany Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Brouwer, Rutger W.
论文数: 0 引用数: 0
h-index: 0
机构:
Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands
Erasmus MC, Ctr Biom, Rotterdam, Netherlands Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Oole, Edwin
论文数: 0 引用数: 0
h-index: 0
机构:
Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands
Erasmus MC, Ctr Biom, Rotterdam, Netherlands Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Shah, Juhi
论文数: 0 引用数: 0
h-index: 0
机构:
McGill Univ, McGill Univ Hlth Ctr, Dept Med, Res Inst, Montreal, PQ, Canada Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Ozdian, Tomas
论文数: 0 引用数: 0
h-index: 0
机构:
Palacky Univ, Fac Med & Dent, Inst Mol & Translat Med, Olomouc, Czech Republic Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Liao, Jie
论文数: 0 引用数: 0
h-index: 0
机构:
McGill Univ, CF Translat Res Ctr, Dept Physiol, Montreal, PQ, Canada Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Martini, Carolina
论文数: 0 引用数: 0
h-index: 0
机构:
McGill Univ, CF Translat Res Ctr, Dept Physiol, Montreal, PQ, Canada Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Radzioch, Danuta
论文数: 0 引用数: 0
h-index: 0
机构:
McGill Univ, McGill Univ Hlth Ctr, Dept Med, Res Inst, Montreal, PQ, Canada Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Hanrahan, John W.
论文数: 0 引用数: 0
h-index: 0
机构:
McGill Univ, McGill Univ Hlth Ctr, Dept Med, Res Inst, Montreal, PQ, Canada
McGill Univ, CF Translat Res Ctr, Dept Physiol, Montreal, PQ, Canada Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands

Scholte, Bob J.
论文数: 0 引用数: 0
h-index: 0
机构:
Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands
Erasmus MC, Sophia Childrens Hosp, Pediat Pulmonol, Rotterdam, Netherlands Erasmus MC, Cell Biol Dept, Rotterdam, Netherlands