Pediatric Bentall procedure for giant ascending aortic aneurysm in Loeys-Dietz syndrome

被引:1
|
作者
Sicim, Huseyin [1 ]
Ulucan, Ali Ertan [1 ]
Yurdakok, Okan [1 ]
Aydemir, Numan Ali [1 ]
机构
[1] Dr Siyami Ersek Thorac & Cardiovasc Surg Training, Dept Pediat Cardiac Surg, Istanbul, Turkiye
关键词
Aortic aneurysm; Bentall procedure; Loeys-Dietz syndrome; REPLACEMENT; MUTATIONS;
D O I
10.4103/apc.apc_22_23
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Ascending aortic aneurysm is very rare in children, and is usually seen in patients with underlying connective tissue disorders such as Marfans and Ehler-Danlos syndrome. Loeys-Dietz syndrome (LDS) is less commonly seen as a cause of ascending aortic aneurysms in children. In this case report, we describe pediatric Bentall procedure, which we successfully performed to a child with LDS (Type I) with giant ascending aortic enlargement and significant aortic regurgitation.
引用
收藏
页码:223 / 225
页数:3
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