Current perspectives of sudden cardiac death management in hypertrophic cardiomyopathy

被引:2
作者
Pu, Lutong [1 ]
Li, Jialin [1 ]
Qi, Weitang [1 ]
Zhang, Jinquan [2 ]
Chen, Hongyu [2 ]
Tang, Zihuan [2 ]
Han, Yuchi [3 ]
Wang, Jie [1 ]
Chen, Yucheng [1 ,4 ]
机构
[1] Sichuan Univ, West China Hosp, Dept Cardiol, Guoxue Xiang 37, Chengdu 610041, Sichuan, Peoples R China
[2] Sichuan Univ, West China Sch Publ Hlth, Chengdu, Sichuan, Peoples R China
[3] Ohio State Univ, Coll Med, Wexner Med Ctr, Columbus, OH USA
[4] Sichuan Univ, West China Hosp, Ctr Rare Dis, Chengdu 610041, Sichuan, Peoples R China
基金
中国国家自然科学基金;
关键词
Hypertrophic cardiomyopathy; Sudden cardiac death; Cardiovascular magnetic resonance; Prognosis; RISK STRATIFICATION; PROGNOSTIC VALUE; GENE-MUTATIONS; PREVENTION; GUIDELINES; CONSEQUENCES; DYSFUNCTION; CARDIOLOGY; SARCOMERE; DIAGNOSIS;
D O I
10.1007/s10741-023-10355-w
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Hypertrophic cardiomyopathy (HCM) is an autosomal dominant disorder characterized by left ventricular hypertrophy. Sudden cardiac death (SCD) is a rare but the most catastrophic complication in patients with HCM. Implantable cardioverter-defibrillators (ICDs) are widely recognized as effective preventive measures for SCD. Individualized risk stratification and early intervention in HCM can significantly improve patient prognosis. In this study, we review the latest findings regarding pathogenesis, risk stratification, and prevention of SCD in HCM patients, highlighting the clinic practice of cardiovascular magnetic resonance imaging for SCD management.
引用
收藏
页码:395 / 404
页数:10
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