Strategies for the Surgical Management of Highly Aggressive Williams Syndrome Aortopathy: A Three Case Report

被引：0
作者：
Nguyen, Stephanie N. [1 ]
Blitzer, David [1 ]
Bouhout, Ismail [1 ]
Vinogradsky, Alice V. [1 ]
Clapcich, Anthony [2 ]
Torres, Alejandro [3 ]
Bacha, Emile A. [1 ]
机构：
[1] New York Presbyterian, Sect Pediat & Congenital Cardiac Surg, Morgan Stanley Childrens Hosp, New York, NY 10032 USA
[2] New York Presbyterian, Dept Pediat Anesthesiol, Morgan Stanley Childrens Hosp, New York, NY USA
[3] New York Presbyterian, Dept Pediat Cardiol, Morgan Stanley Childrens Hosp, New York, NY USA
来源：
PEDIATRIC CARDIOLOGY | 2024年 / 45卷 / 01期
关键词：
Williams syndrome; Aortopathy; Supravalvar aortic stenosis; Thoracic aortic stenosis; SUPRAVALVAR AORTIC-STENOSIS; REPAIR;
D O I：
10.1007/s00246-023-03383-8
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Severe aortopathy in Williams syndrome can sometimes present with an initial ascending aortic pathology, followed in short order by more distal multilevel obstruction and recurrence requiring reintervention. In this series, an early, comprehensive surgical approach using a combination of various access and perfusion strategies yielded excellent long-term results.
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收藏
页码：208 / 212
页数：5
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