Operative repair of right intrathoracic subclavian artery aneurysms in patients with genetic arteriopathy

被引:3
|
作者
French, Bryce L. [1 ]
Menghini, Anthony M. [2 ]
Burke, Christopher R. [3 ]
Byers, Peter H. [4 ]
Shalhub, Sherene [2 ,5 ,6 ]
机构
[1] Kootenai Hlth, Dept Surg, Div Vasc Surg, Coeur DAlene, ID USA
[2] Univ Washington, Sch Med, Div Vasc Surg, Dept Surg, Seattle, WA USA
[3] Univ Washington, Sch Med, Div Cardiac Surg, Dept Surg, Seattle, WA USA
[4] Univ Washington, Dept Lab Med & Pathol, Seattle, WA USA
[5] Oregon Hlth & Sci Univ, Dept Surg, Div Vasc & Endovasc Surg, Portland, OR USA
[6] Oregon Hlth & Sci Univ, Dept Surg, Div Vasc & Endovasc Surg, 3181 SW Sam Jackson Pk Rd,Mail Code OP11, Portland, OR 97239 USA
来源
JOURNAL OF VASCULAR SURGERY CASES INNOVATIONS AND TECHNIQUES | 2023年 / 9卷 / 03期
关键词
Subclavian artery aneurysm; Intrathoracic aneurysm; Peripheral artery aneurysm; Marfan syndrome; Vascular Ehlers Danlos syndrome; MANAGEMENT; DIAGNOSIS;
D O I
10.1016/j.jvscit.2022.11.018
中图分类号
R61 [外科手术学];
学科分类号
摘要
True intrathoracic subclavian artery aneurysms (SCAAs) are rare and have various etiologies. Right intrathoracic SCAAs pose specific anatomic challenges to repair. We present three different operative approaches, open, endovascular, and hybrid repair, for the repair of a right intrathoracic SCAA in three patients with genetic arteriopathy: Marfan syndrome, vascular Ehlers-Danlos syndrome, and unspecified Ehlers-Danlos syndrome, respectively. These cases demonstrate an individualized operative approach based on the genetic diagnosis for each patient presenting with a right intrathoracic SCAA.
引用
收藏
页数:6
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