Budd-Chiari syndrome is a very rare disorder in paediatric age group, which is characterised by narrowing or obstruction of hepatic venous outflow. The obstruction might be thrombotic or non-thrombotic along the course of hepatic venules to junction of inferior vena cava to the right atrium, which leads to abdominal pain in right hypochondrium, hepatomegaly, ascites and portal hypertension. The cause of venous obstruction in children is mainly due to hypercoagulable state. The mean age of Budd-Chiari syndrome is 20-40 years, but here we can see that it occurs in paediatric age group, so good clinical suspicion is required along with investigation to confirm the diagnosis. Traditional approach to the treatment of Budd-Chiari syndrome is systemic thrombolysis or surgical Porto systemic shunt. Recently, successful treatment of Budd-Chiari syndrome is done by endovascular techniques, including angioplasty and stent placement. Here, in this case it shows a successful percutaneous recanalization of complete hepatic vein occlusion by angioplasty and stent placement.
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MIT, Dept Mech Engn, Cambridge, MA 02139 USAMIT, Dept Mech Engn, Cambridge, MA 02139 USA
Li, Chengxi
Li, Rentao
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Tianjin Med Univ, Natl Clin Res Ctr Canc, Dept Hepatobiliary Surg, Canc Inst & Hosp, Tianjin, Peoples R China
Key Lab Canc Prevent & Therapy, Tianjin, Peoples R China
Tianjins Clin Res Ctr Canc, Tianjin 300060, Peoples R ChinaMIT, Dept Mech Engn, Cambridge, MA 02139 USA
Li, Rentao
Zhang, Wei
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Tianjin Med Univ, Natl Clin Res Ctr Canc, Dept Hepatobiliary Surg, Canc Inst & Hosp, Tianjin, Peoples R China
Key Lab Canc Prevent & Therapy, Tianjin, Peoples R China
Tianjins Clin Res Ctr Canc, Tianjin 300060, Peoples R ChinaMIT, Dept Mech Engn, Cambridge, MA 02139 USA
机构:
Nanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Lin, Mengjie
Zhang, Feng
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Nanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zhang, Feng
Wang, Yi
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Wang, Yi
Zhang, Bin
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zhang, Bin
Zhang, Wei
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zhang, Wei
Zou, Xiaoping
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zou, Xiaoping
Zhang, Ming
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zhang, Ming
Zhuge, Yuzheng
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
机构:
Seth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India
King Edward Mem Hosp, Bombay 400012, Maharashtra, IndiaSeth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India
Patil, Pritam
Deshmukh, Hemant
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机构:Seth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India
Deshmukh, Hemant
Popat, Bhavesh
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机构:Seth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India
Popat, Bhavesh
Rathod, Krantikumar
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机构:Seth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India
机构:
MIT, Dept Mech Engn, Cambridge, MA 02139 USAMIT, Dept Mech Engn, Cambridge, MA 02139 USA
Li, Chengxi
Li, Rentao
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机构:
Tianjin Med Univ, Natl Clin Res Ctr Canc, Dept Hepatobiliary Surg, Canc Inst & Hosp, Tianjin, Peoples R China
Key Lab Canc Prevent & Therapy, Tianjin, Peoples R China
Tianjins Clin Res Ctr Canc, Tianjin 300060, Peoples R ChinaMIT, Dept Mech Engn, Cambridge, MA 02139 USA
Li, Rentao
Zhang, Wei
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机构:
Tianjin Med Univ, Natl Clin Res Ctr Canc, Dept Hepatobiliary Surg, Canc Inst & Hosp, Tianjin, Peoples R China
Key Lab Canc Prevent & Therapy, Tianjin, Peoples R China
Tianjins Clin Res Ctr Canc, Tianjin 300060, Peoples R ChinaMIT, Dept Mech Engn, Cambridge, MA 02139 USA
机构:
Nanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Lin, Mengjie
Zhang, Feng
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Nanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zhang, Feng
Wang, Yi
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Wang, Yi
Zhang, Bin
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zhang, Bin
Zhang, Wei
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zhang, Wei
Zou, Xiaoping
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zou, Xiaoping
Zhang, Ming
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
Zhang, Ming
Zhuge, Yuzheng
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Nanjing Univ, Med Sch, Affiliated Drum Tower Hosp, Dept Gastroenterol, 321 Zhongshan Rd, Nanjing 210008, Jiangsu, Peoples R ChinaNanjing Med Univ, Drum Tower Clin Med Sch, Nanjing, Jiangsu, Peoples R China
机构:
Seth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India
King Edward Mem Hosp, Bombay 400012, Maharashtra, IndiaSeth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India
Patil, Pritam
Deshmukh, Hemant
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机构:Seth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India
Deshmukh, Hemant
Popat, Bhavesh
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机构:Seth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India
Popat, Bhavesh
Rathod, Krantikumar
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机构:Seth GS Med Coll, Dept Radiol, Bombay 400012, Maharashtra, India