Outcomes of cochlear implantation in Usher syndrome: a systematic review

被引：2

作者：

Cornwall, Hannah Louisa ^{[1
]}

Lam, Chon Meng ^{[1
]}

Chaudhry, Daoud ^{[2
]}

Muzaffar, Jameel ^{[3
,4
]}

Monksfield, Peter ^{[4
]}

Bance, Manohar L. ^{[3
,5
]}

机构：

[1] Cardiff & Vale Univ Hlth Board, Cardiff, Wales

[2] Univ Birmingham, Coll Med & Dent Sci, Birmingham, England

[3] Univ Cambridge, Dept Clin Neurosci, Box 165,Level 3,Block Cambridge Biomed Campus, Cambridge CB2 0QQ, England

[4] Univ Hosp Birmingham NHS Fdn Trust, Dept Otolaryngol, Birmingham, England

[5] Cambridge Univ Hosp NHS Fdn Trust, Addenbrookes Hosp, Dept Otolaryngol, Cambridge, England

来源：

EUROPEAN ARCHIVES OF OTO-RHINO-LARYNGOLOGY | 2024年 / 281卷 / 03期

关键词：

Usher syndrome; Cochlear implant; Hearing loss; Quality of life; NEUROPATHY SPECTRUM DISORDER; ISOLATED AUDITORY NEUROPATHY; BRAIN-STEM RESPONSE; SPEECH-PERCEPTION; EVOKED POTENTIALS; CHILDREN; PERFORMANCE; MATURATION; MANAGEMENT; USERS;

D O I：

10.1007/s00405-023-08304-2

中图分类号：

R76 [耳鼻咽喉科学];

学科分类号：

100213 ;

摘要：

PurposeThis study is a systematic review of the literature which seeks to evaluate auditory and quality of life (QOL) outcomes of cochlear implantation in patients with Usher syndrome.MethodsSystematic review of studies indexed in Medline via PubMed, Ovid EMBASE, Web of Science, CENTRAL and clinicaltrials.gov was performed up to March 9th 2022, conducted in accordance with the PRISMA statement. Patient demographics, comorbidity, details of cochlear implantation, auditory, and QOL outcomes were extracted and summarized.Results33 studies reported over 217 cochlear implants in 187 patients with Usher syndrome, comprising subtypes 1 (56 patients), 2 (9 patients), 3 (23 patients), and not specified (99 patients). Auditory outcomes included improved sound detection, speech perception, and speech intelligibility. QOL outcomes were reported for 75 patients, with benefit reported in the majority.ConclusionsMany patients with Usher syndrome develop improved auditory outcomes after cochlear implantation with early implantation being an important factor.

引用

页码：1115 / 1129

页数：15

共 48 条

[1] Simultaneous bilateral cochlear implantation in a five-month-old child with Usher syndrome [J].