Benign to Malignant Hepatic Lesion Transformation in Abernethy Malformation

被引：0

作者：

Tom, Chloe K. ^{[1
]}

Ter-Oganesyan, Ramon ^{[2
]}

Shefali, Chopra ^{[3
]}

Kaur, Navpreet ^{[4
]}

Pace, Jordan L. ^{[5
]}

Rastegarpour, Ali ^{[6
]}

Genyk, Yuri ^{[7
]}

Kahn, Jeffrey A. ^{[8
,9
]}

机构：

[1] Univ Southern Calif, Div Gastrointestinal & Liver Dis, Los Angeles, CA 90007 USA

[2] Univ Southern Calif, Dept Radiol, Div Vasc & Intervent Radiol, Los Angeles, CA USA

[3] Univ Southern Calif, Dept Pathol, Los Angeles, CA USA

[4] Univ Southern Calif, Dept Surg, Los Angeles, CA USA

[5] Calif Univ Sci & Med Colton, Colton, CA USA

[6] Univ Southern Calif Los Angeles, Dept Diagnost Radiol, Los Angeles, CA USA

[7] Univ Southern Calif Los Angeles, Div Hepatobiliary Pancreat & Abdominal Organ Trans, Los Angeles, CA USA

[8] Univ Southern Calif Los Angeles, Div Gastrointestinal & Liver Dis, Los Angeles, CA USA

[9] Univ Southern Calif Los Angeles, Liver Transplant Program, Los Angeles, CA USA

来源：

ACG CASE REPORTS JOURNAL | 2024年 / 11卷 / 04期

关键词：

Abernethy malformation; congenital extrahepatic porosystemic shunt; hepatocellular carcinoma; focal nodular hyperplasia; hepatocellular adenoma; HEPATOCELLULAR-CARCINOMA; PORTOSYSTEMIC SHUNTS;

D O I：

10.14309/crj.0000000000001307

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

Abernethy malformation or congenital extrahepatic portosystemic shunt is an extremely rare condition whereby the portomesenteric blood drains into a systemic vein and bypasses the liver through a complete or partial shunt. Severe complications include hyperammonemia and encephalopathy, benign and malignant liver tumors, and hepatopulmonary syndrome. We describe a case where a female adult diagnosed with congenital extrahepatic portosystemic shunt subsequently developed focal nodular hyperplasia and then hepatocellular carcinoma.

引用

页数：4

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