Clinical Management of Brugada Syndrome: Commentary From the Experts

被引:3
作者
Cutler, Michael J. [1 ,2 ]
Eckhardt, Lee L. [3 ]
Kaufman, Elizabeth S. [4 ]
Arbelo, Elena [5 ,6 ,7 ]
Behr, Elijah R. [8 ,9 ,10 ]
Brugada, Pedro [11 ,12 ]
Cerrone, Marina [13 ]
Crotti, Lia [14 ,15 ,16 ]
Deasmundis, Carlo [17 ]
Gollob, Michael H. [18 ]
Horie, Minoru [19 ]
Huang, David T. [20 ]
Krahn, Andrew D. [21 ]
London, Barry [22 ,23 ]
Lubitz, Steven A. [24 ]
Mackall, Judith A. [25 ]
Nademanee, Koonlawee [26 ,27 ]
Perez, Marco V. [28 ]
Probst, Vincent [29 ]
Roden, Dan M. [30 ,31 ,32 ]
Sacher, Frederic [33 ]
Sarquella-Brugada, Georgia [34 ,35 ]
Scheinman, Melvin M. [36 ]
Shimizu, Wataru [37 ]
Shoemaker, Benjamin [38 ]
Sy, Raymond W. [39 ,40 ]
Watanabe, Atsuyuki [41 ]
Wilde, Arthur A. M. [42 ,43 ]
机构
[1] Eccles Outpatient Care Ctr, Intermt Heart Inst, Intermt Med Ctr, Cardiac Electrophysiol,Intermt Hlth, 5169 Cottonwood St,Ste 510, Murray, UT 84107 USA
[2] Intermt Heart Inst, Intermt Med Ctr, Salt Lake City, UT USA
[3] Univ Wisconsin, Dept Med, Cellular & Mol Arrhythmia Res Program, Div CVM, Madison, WI USA
[4] Case Western Reserve Univ, Heart & Vasc Ctr, Metrohlth Campus, Cleveland, OH USA
[5] Univ Barcelona, Hosp Clin, Cardiol Dept, Arrhythmia Sect, Barcelona, Spain
[6] Ctr Invest Biomed Red Enfermedades Cardiovasc CIBE, Madrid, Spain
[7] Inst Invest August Pi I Sunyer, IDIBAPS, Barcelona, Spain
[8] St Georges Univ London, Cardiol Sect, Cardiovasc Clin Acad Grp, London, England
[9] St Georges Univ Hosp NHS Fdn Trust, London, England
[10] Mayo Clin Healthcare, London, England
[11] UZ Brussel VUB, Cardiovasc Div, Brussels, Belgium
[12] Helicopteros Sanitarios Hosp HSH, Arrhythmia Unit, Malaga 29603, Spain
[13] NYU, Leon H Charney Div Cardiol, Grossman Sch Med, New York, NY USA
[14] Univ Milano Bicocca, Dept Med & Surg, Milan, Italy
[15] Ist Auxol Italiano IRCCS, Ctr Cardiac Arrhythmias Genet Origin, Milan, Italy
[16] Ist Auxol Italiano IRCCS, Lab Cardiovasc Genet, Milan, Italy
[17] Vrije Univ Brussel, Univ Ziekenhuis Brussel, Postgrad Program Cardiac Electrophysiol & Pacing, Heart Rhythm Management Ctr,European Reference Net, Brussels, Belgium
[18] Univ Hlth Network, Toronto Gen Hosp, Peter Munk Cardiac Ctr, Div Cardiol, Toronto, ON, Canada
[19] Shiga Univ Med Sci, Dept Cardiovasc Med, Otsu, Japan
[20] Univ Rochester, Med Ctr, Rochester, NY 14642 USA
[21] Univ British Columbia, Ctr Cardiovasc Innovat, Div Cardiol, Vancouver, BC, Canada
[22] Univ Iowa, Carver Coll Med, Dept Internal Med, Div Cardiovasc Med, Iowa City, IA USA
[23] Univ Iowa, Abboud Cardiovasc Res Ctr, Carver Coll Med, Iowa City, IA USA
[24] Massachusetts Gen Hosp, Demoulas Ctr Cardiac Arrhythmias, Boston, MA USA
[25] Case Western Reserve Univ, Univ Hosp Harrington Heart & Vasc Inst, Dept Med, Div Cardiol,Sch Med, Cleveland, OH USA
[26] Chulalongkorn Univ, Fac Med, Ctr Excellence Arrhythmia Res, Dept Med, Bangkok, Thailand
[27] Bumrungrad Hosp, Pacific Rim Electrophysiol Res Inst, Bangkok, Thailand
[28] Stanford Univ, Stanford Ctr Inherited Cardiovasc Dis, Stanford, CA USA
[29] Univ Nantes, CHU Nantes, CNRS, INSERM,Inst Thorax,Serv Cardiol, Nantes, France
[30] Vanderbilt Univ, Dept Med, Med Ctr, Nashville, TN USA
[31] Vanderbilt Univ, Dept Pharmacol, Med Ctr, Nashville, TN USA
[32] Vanderbilt Univ, Dept Biomed Informat, Med Ctr, Nashville, TN USA
[33] Bordeaux Univ Hosp, Arrhythmia Dept, IHU LIRYC, Pessac, France
[34] Univ Barcelona, Hosp St Joan Deu, Inherited Cardiac Dis & Sudden Death Unit, Pediat Arrhythmias, Barcelona, Spain
[35] Inst Recerca St Joan Deu, Arritmies Pediat Cardiol Genet & Mort Sobtada, Malalties Cardiovasc Desenvolupament, Barcelona 08950, Spain
[36] Univ Calif San Francisco, Sect Cardiac Electrophysiol, Div Cardiol, San Francisco, CA USA
[37] Nippon Med Sch, Grad Sch Med, Dept Cardiovasc Med, Tokyo, Japan
[38] Vanderbilt Univ, Med Ctr, Dept Med, Div Cardiovasc Med, Nashville, TN USA
[39] Univ Sydney, Fac Med & Heath, Sydney, Australia
[40] Royal Prince Alfred Hosp, Dept Cardiol, Sydney, Australia
[41] Natl Hosp Org Okayama Med Ctr, Dept Cardiol, Okayama, Japan
[42] Univ Amsterdam, Dept Cardiol, Amsterdam, Netherlands
[43] Amsterdam Cardiovasc Sci, Heart Failure & Arrhythmias, Amsterdam, Netherlands
基金
美国国家卫生研究院;
关键词
Brugada Syndrome; sudden cardiac arrest; syncope; ventricular fibrillation; ST SEGMENT ELEVATION; SUDDEN CARDIAC DEATH; PROGRAMMED ELECTRICAL-STIMULATION; IMPLANTABLE LOOP RECORDER; RISK STRATIFICATION; ELECTROCARDIOGRAPHIC PARAMETERS; CONSENSUS CONFERENCE; PROGNOSTIC VALUE; SCORE MODEL; DIAGNOSIS;
D O I
10.1161/CIRCEP.123.012072
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Although there is consensus on the management of patients with Brugada Syndrome with high risk for sudden cardiac arrest, asymptomatic or intermediate-risk patients present clinical management challenges. This document explores the management opinions of experts throughout the world for patients with Brugada Syndrome who do not fit guideline recommendations. Four real-world clinical scenarios were presented with commentary from small expert groups for each case. All authors voted on case-specific questions to evaluate the level of consensus among the entire group in nuanced diagnostic and management decisions relevant to each case. Points of agreement, points of controversy, and gaps in knowledge are highlighted.
引用
收藏
页码:52 / 66
页数:15
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