A "Leopard Man" Aspect on 18F-FDG PET/CT Revealing a VEXAS Syndrome

被引：4

作者：

Fagart, Alexandre ^{[1
]}

Quemeneur, Thomas ^{[2
]}

Collet, Guillaume ^{[1
]}

Demailly, Franck ^{[1
]}

Rousselin, Clementine ^{[2
]}

机构：

[1] Hosp Ctr Valenciennes, Dept Nucl Med, 114 Ave Desandrouin, F-59300 Valenciennes, France

[2] Hosp Ctr Valenciennes, Dept Nephrol & Internal Med, Valenciennes, France

来源：

CLINICAL NUCLEAR MEDICINE | 2023年 / 48卷 / 01期

关键词：

VEXAS syndrome; polyarteritis nodosa; myelodysplastic syndrome; FDG PET/CT; autoinflammatory diseases; BONE-MARROW INVOLVEMENT; MEDIATED FDG UPTAKE;

D O I：

10.1097/RLU.0000000000004443

中图分类号：

R8 [特种医学]; R445 [影像诊断学];

学科分类号：

1002 ; 100207 ; 1009 ;

摘要：

VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome is an adult-onset autoinflammatory disease caused by somatic UBA1 mutations first described in 2020. Most of these patients met clinical criteria for an inflammatory syndrome (relapsing polychondritis, Sweet syndrome, polyarteritis nodosa, or giant-cell arteritis) or a hematologic condition (myelodysplastic syndrome or multiple myeloma) or both. We described here an FDG PET/CT "leopard man " appearance, with abnormal marrow recruitment the findings, in a 70-year-old man diagnosed with a VEXAS syndrome.

引用

页码：E33 / E34

页数：2

共 50 条

[1] 18F-FDG PET/CT Findings in a Patient With Sweet Syndrome Associated With Myelodysplastic Syndrome
Dong, Aisheng
Wang, Yang
Gao, Lei
Zuo, Changjing
CLINICAL NUCLEAR MEDICINE, 2013, 38 (12) : E54 - E57
[2] 18F-FDG PET/CT in the evaluation of POEMS syndrome
Alberti, M. A.
Martinez-Yelamos, S.
Fernandez, A.
Vidaller, A.
Narvaez, J. A.
Cano, L. M.
Gamez, C.
Martinez-Matos, J. A.
EUROPEAN JOURNAL OF RADIOLOGY, 2010, 76 (02) : 180 - 182
[3] Richter's syndrome: Utility of 18F-FDG PET/CT
Garcia Vicente, A. M.
Jimenez Londono, G. A.
Hernandez Ruiz, B.
Soriano Castrejon, A.
REVISTA ESPANOLA DE MEDICINA NUCLEAR E IMAGEN MOLECULAR, 2013, 32 (02): : 102 - 104
[4] 18F-FDG PET or PET/CT in Mantle Cell Lymphoma
Albano, Domenico
Treglia, Giorgio
Gazzilli, Maria
Cerudelli, Elisabetta
Giubbini, Raffaele
Bertagna, Francesco
CLINICAL LYMPHOMA MYELOMA & LEUKEMIA, 2020, 20 (07) : 422 - 430
[5] Serial 18F-FDG PET/CT Revealing Mixed Histiocytosis in a Pediatric Patient
Singh, Karan
Lau, Loretta
Wegner, Eva A.
Rossleigh, Monica A.
Shon, Ivan Ho
CLINICAL NUCLEAR MEDICINE, 2024, 49 (10) : e518 - e520
[6] Infectious Aortitis on 18F-FDG PET/CT
El Hoyek, Nadine
Chen, Wengen
Aktay, Recai
CLINICAL NUCLEAR MEDICINE, 2024, 49 (09) : 866 - 867
[7] Hepatic Schwannoma on 18F-FDG PET/CT
Liu, Yachao
Xu, Baixuan
CLINICAL NUCLEAR MEDICINE, 2020, 45 (10) : 808 - 810
[8] 18F-FDG PET/CT in the Evaluation of Bing-Neel Syndrome
Illarramendil, Odile Ajuria
Flynt, Lesley
Wong, Franklin
JOURNAL OF NUCLEAR MEDICINE TECHNOLOGY, 2019, 47 (04) : 343 - 344
[9] Diagnostic Value of 18F-FDG PET/CT in Comparison to Bone Scintigraphy, CT and 18F-FDG PET for the Detection of Bone Metastasis
Liu, Ning-Bo
Zhu, Lei
Li, Ming-Huan
Sun, Xiao-Rong
Hu, Man
Huo, Zong-Wei
Xu, Wen-Gui
Yu, Jin-Ming
ASIAN PACIFIC JOURNAL OF CANCER PREVENTION, 2013, 14 (06) : 3647 - 3652
[10] Measurement Repeatability of 18F-FDG PET/CT Versus 18F-FDG PET/MRI in Solid Tumors of the Pelvis
Fraum, Tyler J.
Fowler, Kathryn J.
Crandall, John P.
Laforest, Richard A.
Salter, Amber
An, Hongyu
Jacobs, Michael A.
Grigsby, Perry W.
Dehdashti, Farrokh
Wahl, Richard L.
JOURNAL OF NUCLEAR MEDICINE, 2019, 60 (08) : 1080 - 1086

← 1 2 3 4 5 →