Allogeneic hematopoietic stem cell transplantation for juvenile myelomonocytic leukemia with intestinal Behçet's disease: A case report

被引：0

作者：

Liu, Chang ^{[1
]}

Fu, Caihong ^{[1
]}

Guo, Xuemei ^{[1
]}

Rong, Liucheng ^{[1
]}

Li, Jian ^{[1
]}

Fang, Yongjun ^{[1
,2
]}

机构：

[1] Nanjing Med Univ, Childrens Hosp, Dept Hematol & Oncol, Nanjing, Peoples R China

[2] Nanjing Med Univ, Dept Hematol & Oncol, Childrens Hosp, Nanjing 210008, Peoples R China

来源：

INTERNATIONAL JOURNAL OF RHEUMATIC DISEASES | 2024年 / 27卷 / 01期

基金：

中国国家自然科学基金; 中国博士后科学基金;

关键词：

allogeneic hematopoietic stem cell transplantation; autoimmunity; Behcet's disease; juvenile myelomonocytic leukemia; myeloid malignancy;

D O I：

10.1111/1756-185X.14882

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Behcet's disease (BD) is a rare condition that is seldom associated with hematological malignancies. In this case report, we present the unique case of a 7-year-old girl diagnosed with juvenile myelomonocytic leukemia (JMML) and intestinal BD. The patient received allogeneic hematopoietic stem cell transplantation (allo-HSCT), which resulted in complete remission of both JMML and BD. Our findings suggest that allo-HSCT may be a feasible treatment option for JMML patients with coexisting BD, and holds promise for achieving remission of both illnesses. However, further clinical investigations are needed to validate these findings.

引用

页数：4

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