An Adult Male With Sporadic Creutzfeldt-Jakob Disease: A Case Report

被引：0

作者：

Alfandy, Fnu ^{[1
]}

Salari-Namin, Hamid Reza ^{[2
]}

Constan, Dennis Kaighn ^{[3
]}

机构：

[1] Stanford Hlth Care Neurosci Serv Line Stanford, Adv Practice Provider Program manager, Stanford, CA 94305 USA

[2] Eisenhower Hlth Rancho Mirage, Vasc neurologist, Rancho Mirage, CA USA

[3] Eisenhower Hlth, Clin pharmacist, Rancho Mirage, CA USA

来源：

JNP- THE JOURNAL FOR NURSE PRACTITIONERS | 2023年 / 19卷 / 05期

关键词：

Creutzfeldt-Jakob disease; intestinal pseudo-obstruction; neurodegenerative disease; prion disease;

D O I：

10.1016/j.nurpra.2022.104533

中图分类号：

R47 [护理学];

学科分类号：

1011 ;

摘要：

Creutzfeldt-Jakob disease (CJD) is a transmissible, progressive, neurogenerative disease that carries a uni-formly poor prognosis. It is caused by an accumulation of misfolded prions that affect the structural conformation of the surrounding proteins. Sporadic CJD is the most common form of CJD, accounting for 85% to 95% of all CJD cases. The rarity of CJD makes its diagnosis challenging, and it can mimic other neurologic conditions. The CJD International Surveillance Network diagnostic criteria include clinical features and diagnostic findings with which health care providers should be familiar. The purpose of this report is to present a case of postmortem definite CJD. (c) 2022 Elsevier Inc. All rights reserved.

引用

页数：4

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