Beyond the Lungs-Emerging Challenges in Adult Cystic Fibrosis Care

被引：5
|
作者：
Mulrennan, Siobhain [1 ]
Sapru, Karuna [2 ]
Tewkesbury, Daniel [2 ]
Jones, Andrew M. [2 ,3 ]
机构：
[1] Sir Charles Gairdner Hosp, Perth, Australia
[2] Wythenshawe Hosp, Manchester Adult Cyst Fibrosis Ctr, Manchester, England
[3] Wythenshawe Hosp, Manchester Adult Cyst Fibrosis Ctr, Southmoor Rd, Manchester M23 9LT, England
来源：
SEMINARS IN RESPIRATORY AND CRITICAL CARE MEDICINE | 2023年 / 44卷 / 02期
关键词：
cystic fibrosis; CFTR modulators; aging; malignancy; cardiovascular disease; bone health; RISK-FACTORS; VERTEBRAL FRACTURES; LIVER-DISEASE; DEPRESSION; PREGNANCY; HEALTH; WOMEN; PREVALENCE; CFTR; ASSOCIATION;
D O I：
10.1055/s-0042-1758734
中图分类号：
R4 [临床医学];
学科分类号：
1002 ; 100602 ;
摘要：
Cystic fibrosis (CF) is a multisystem disease. This article provides an up-to-date review of many of the nonrespiratory complications of CF, including mental health issues, nutritional and gastrointestinal problems, fertility issues, diabetes mellitus, bone health and musculoskeletal problems, liver disease, renal problems, and risk of malignancy. It highlights the recent impact of new therapies, including CF transmembrane conductance regulator modulators, on the nonrespiratory complications of CF and provides insights into the potential challenges faced by an aging population of adults with CF and their caregivers, including the potential future risk for cardiovascular disease.
引用
收藏
页码：307 / 313
页数：7
相关论文
共 50 条
  • [1] Transition to adult care in cystic fibrosis: The challenges and the structure
    Singh, Jagdev
    Towns, Susan
    Jayasuriya, Geshani
    Hunt, Sharon
    Simonds, Sharon
    Boyton, Christie
    Middleton, Anna
    Kench, Andrea
    Pandit, Chetan
    Keatley, Lucy R.
    Chien, Jimmy
    Bishop, Jennifer
    Song, Yang
    Robinson, Paul
    Selvadurai, Hiran
    Middleton, Peter G.
    Fitzgerald, Dominic A.
    PAEDIATRIC RESPIRATORY REVIEWS, 2022, 41 : 23 - 29
  • [2] BEYOND THE LUNGS: WHY FERTILITY MATTERS IN THE CARE OF INDIVIDUALS WITH CYSTIC FIBROSIS
    Ladores, Sigrid L.
    PEDIATRIC PULMONOLOGY, 2019, 54 : S56 - S57
  • [3] Ageing with cystic fibrosis: Classical and emerging comorbidities in adults with cystic fibrosis
    Regard, L.
    Lafoeste, H.
    Martin, C.
    Chassagnon, G.
    Burgel, P. -R.
    REVUE DE PNEUMOLOGIE CLINIQUE, 2018, 74 (05) : 279 - 291
  • [4] Emerging Nonpulmonary Complications for Adults With Cystic Fibrosis Adult Cystic Fibrosis Series
    Chin, Melanie
    Brennan, Amanda L.
    Bell, Scott C.
    CHEST, 2022, 161 (05) : 1211 - 1224
  • [5] Adult Care in Cystic Fibrosis
    Elborn, J. Stuart
    SEMINARS IN RESPIRATORY AND CRITICAL CARE MEDICINE, 2019, 40 (06) : 857 - 868
  • [6] The dance of cystic fibrosis: Experiences of living with cystic fibrosis as an adult
    Varilek, Brandon M.
    Isaacson, Mary J.
    JOURNAL OF CLINICAL NURSING, 2020, 29 (17-18) : 3553 - 3564
  • [7] Update on Key Emerging Challenges in Cystic Fibrosis
    Jennings, Mark T.
    Riekert, Kristin A.
    Boyle, Michael P.
    MEDICAL PRINCIPLES AND PRACTICE, 2014, 23 (05) : 393 - 402
  • [8] The Changing Epidemiology of Cystic Fibrosis The Implications for Adult Care
    Burgel, Pierre-Regis
    Burnet, Esperie
    Regard, Lucile
    Martin, Clemence
    CHEST, 2023, 163 (01) : 89 - 99
  • [9] SUCCESSFUL RETRANSPLANTATION OF THE HEART AND LUNGS IN AN ADULT WITH CYSTIC-FIBROSIS
    MADDEN, BP
    KHAGHANI, A
    YACOUB, M
    JOURNAL OF THE ROYAL SOCIETY OF MEDICINE, 1991, 84 (09) : 561 - 561
  • [10] Emerging pharmacotherapies in cystic fibrosis
    McElvaney, Oliver J.
    Gunaratnam, Cedric
    McElvaney, Oisin Fiachra
    Bagwe, Isha
    Reeves, Emer P.
    McElvaney, Noel G.
    EXPERT REVIEW OF RESPIRATORY MEDICINE, 2018, 12 (10) : 843 - 855
12345