Malignant Peripheral Nerve Sheath Tumor Arising from Small Bowel Mesentery: an Extremely Rare Case with Review of Literature

被引：1

作者：

Zaheer, Samreen ^{[1
]}

Khosla, Divya ^{[1
]}

Gupta, Vikas ^{[2
]}

Nada, Ritambhra ^{[3
]}

Kumar, Divyesh ^{[1
]}

Kapoor, Rakesh ^{[1
]}

机构：

[1] Postgrad Inst Med Educ & Res PGIMER, Reg Canc Ctr, Dept Radiotherapy, Chandigarh, India

[2] Postgrad Inst Med Educ & Res, Dept Surg Gastroenterol, Chandigarh, India

[3] Postgrad Inst Med Educ & Res, Dept Histopathol, Chandigarh, India

来源：

JOURNAL OF GASTROINTESTINAL CANCER | 2023年 / 54卷 / 01期

关键词：

Small bowel; Mesentery; Malignant Peripheral nerve sheath tumor (MPNST);

D O I：

10.1007/s12029-021-00753-4

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

Purpose Malignant peripheral nerve sheath tumor (MPNST) of small bowel mesentery is a rare tumor. We report a rare case of MPNST of small bowel mesentery in a patient without neurofibromatosis (NF). Methods A 50-year-old male, with no features suggestive of NF1, presented to us with complaints of pain abdomen. Contrast-enhanced computed tomography (CECT) of the abdomen revealed a mass in the infrarenal region. On laparotomy, mass was seen to be arising from the mesentery of the jejunum. En-bloc resection of the tumor was done, and histopathological examination was suggestive of malignant peripheral nerve sheath tumor of the small bowel mesentery. Result Patient received adjuvant external beam radiotherapy to a dose of 50.4 Gy to the tumor bed. The patient was planned for chemotherapy but absconded and later came with recurrence. The patient finally succumbed to disease. Conclusion Surgery is the mainstay of treatment. Adjuvant treatment should be based on histopathological report.

引用

页码：259 / 263

页数：5