Left Ventricular Noncompaction Cardiomyopathy in 2 Siblings With Underlying Tetralogy of Fallot: A Case Report

被引：0
作者：
Abbaszadeh, Reza [1 ]
Naderi, Fatemeh [1 ]
Tatari, Hassan [1 ]
Tabar, Yaser Tolouei [1 ]
机构：
[1] Iran Univ Med Sci, Rajaie Cardiovasc Med & Res Inst, Tehran, Iran
来源：
IRANIAN HEART JOURNAL | 2024年 / 25卷 / 01期
关键词：
Left ventricular noncompaction cardiomyopathy; Tetralogy of Fallot; Congenital cardiac abnormality; NON-COMPACTION; MYOCARDIUM; CLASSIFICATION;
D O I：
暂无
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Tetralogy of Fallot (TOF) is one of the most common congenital heart diseases. Family recurrence provides strong evidence for the involvement of a genetic component in the susceptibility to TOF. The role of genetic factors is supported by the increased risk of firstdegree relatives of patients with TOF. The clinical course of this disease is unclear and unpredictable. We herein describe 2 siblings suffering from TOF with left ventricular noncompaction cardiomyopathy (LVNC) and their clinical course and treatment. LVNC is a rare disease known by prominent trabeculation of the ventricles and reduced systolic function. LVNC can manifest itself in a wide spectrum of symptoms overlapping with other cardiac diagnoses. Familial patterns of disease development and coexistence of cardiac abnormalities are also reported.
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页码：98 / 105
页数：8
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