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Univ Claude Bernard Lyon 1, Univ Lyon, Hosp Civils Lyon,Louis Pradel Hosp,UMR754,ERN LUN, Natl Reference Coordinating Ctr Rare Pulm Dis,IVP, Lyon, France Univ Claude Bernard Lyon 1, Univ Lyon, Hosp Civils Lyon,Louis Pradel Hosp,UMR754,ERN LUN, Natl Reference Coordinating Ctr Rare Pulm Dis,IVP, Lyon, France