Supradiaphragmatic origin of the celiac trunk leading to median arcuate ligament syndrome with superior mesenteric artery involvement

被引:0
作者
Rama, Martina [1 ]
Nasser, Wissam [1 ]
Palvannan, Prashanth [1 ]
Belko, Sara [2 ]
Dimuzio, Paul [1 ]
Palazzo, Francesco [1 ,3 ]
机构
[1] Thomas Jefferson Univ, Sidney Kimmel Med Coll, Dept Surg, Philadelphia, PA USA
[2] Thomas Jefferson Univ, Jefferson Hlth Design Lab, Philadelphia, PA USA
[3] Thomas Jefferson Univ, Sidney Kimmel Med Coll, Dept Surg, 1100 Walnut St, 5th Floor, Philadelphia, PA 19107 USA
来源
JOURNAL OF VASCULAR SURGERY CASES INNOVATIONS AND TECHNIQUES | 2024年 / 10卷 / 01期
关键词
Dunbar syndrome; MAL; MALS; Median arcuate ligament; Median arcuate ligament syndrome; Supradiaphragmatic celiac trunk; Supradiaphragmatic SMA; Two-vessel MALS;
D O I
10.1016/j.jvscit.2023.101315
中图分类号
R61 [外科手术学];
学科分类号
摘要
Median arcuate ligament (MAL) syndrome (MALS) is a rare condition caused by compression of the celiac artery by the MAL. Symptoms include abdominal pain, nausea, and weight loss. Rarely, the MAL can compress both the celiac artery and the superior mesenteric artery (SMA). We describe the case of a young man with MALS involving the celiac artery and SMA. Laparoscopic release of the MAL was performed, and the patient had resolution of his symptoms at 6 months of follow-up. A review of the literature identified only six cases of MALS involving the SMA and celiac artery, making this a rare occurrence. (J Vasc Surg Cases Innov Tech 2024;10:101315.)
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页数:4
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