A case of acute liver failure caused by Budd-Chiari syndrome salvaged by brain-dead donor liver transplantation

被引：0

作者：

Kimura, Kiwamu ^{[1
]}

Osaki, Akihiko ^{[1
]}

Hirata, Yoshihiro ^{[2
]}

Egawa, Hiroto ^{[2
]}

Kogiso, Tomomi ^{[3
]}

Nakamura, Gen ^{[4
]}

Hashidate, Hideki ^{[5
]}

Wakabayashi, Takuya ^{[1
]}

Sato, Munehiro ^{[1
]}

Waguri, Nobuo ^{[1
]}

机构：

[1] Niigata City Gen Hosp, Dept Gastroenterol & Hepatol, 463-7 Shumoku,Chuo Ku, Niigata 9501197, Japan

[2] Tokyo Womens Med Univ, Inst Gastroenterol, Dept Surg, Tokyo, Japan

[3] Tokyo Womens Med Univ, Inst Gastroenterol, Dept Internal Med, Tokyo, Japan

[4] Niigata City Gen Hosp, Dept Nephrol & Rheumatol, Niigata, Japan

[5] Niigata City Gen Hosp, Dept Diagnost Pathol, Niigata, Japan

来源：

CLINICAL JOURNAL OF GASTROENTEROLOGY | 2024年 / 17卷 / 01期

关键词：

Budd-Chiari syndrome; Acute liver failure; Liver transplantation; On-line hemodiafiltration; Myeloproliferative neoplasm; HEPATIC-ENCEPHALOPATHY; THROMBOSIS; PATHOPHYSIOLOGY; CLASSIFICATION; HYPERTENSION; OBSTRUCTION; THERAPY;

D O I：

10.1007/s12328-023-01863-1

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

A 24-year-old man was admitted to our hospital with abdominal distension. He was found to have acute liver failure and diagnosed with Budd-Chiari syndrome based on angiography and liver biopsy. Liver transplantation was deemed necessary when angiography showed extensive thrombotic occlusion of the hepatic veins and liver biopsy revealed submassive hepatic necrosis. The patient was found to have the JAK2V617F mutation, indicating a myeloproliferative neoplasm as the background disease. He developed hepatic encephalopathy but remained conscious on on-line hemodiafiltration. Brain-dead donor liver transplantation was performed on hospital day 30. Since then, the patient has remained well.

引用

页码：84 / 92

页数：9

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