Esophageal lung, pulmonary artery sling and congenital tracheal stenosis: A case report

被引：0

作者：

Liang, Norah E. ^{[1
,7
]}

Kim, Grace S. ^{[2
]}

Gugig, Roberto ^{[3
]}

Ma, Michael ^{[4
]}

Coll, Ana ^{[5
]}

Sidell, Douglas ^{[2
,6
]}

Bruzoni, Matias ^{[1
,6
]}

机构：

[1] Stanford Univ, Div Pediat Surg, Stanford, CA 94114 USA

[2] Stanford Univ, Div Pediat Otolaryngol, Stanford, CA 94305 USA

[3] Stanford Univ, Div Pediat Gastroenterol, Stanford, CA USA

[4] Stanford Univ, Div Pediat Cardiac Surg, Stanford, CA USA

[5] Univ Calif San Francisco, Div Cardiol, Fresno, CA USA

[6] Pediat Aerodigest & Airway Reconstruct Ctr, Stanford, CA 94305 USA

[7] Stanford Univ, Div Pediat Surg, Sch Med, 453 Quarry Rd, Stanford, CA 94305 USA

来源：

JOURNAL OF PEDIATRIC SURGERY CASE REPORTS | 2024年 / 101卷

关键词：

Esophageal lung; Pulmonary artery sling; Tracheal stenosis; Case report;

D O I：

10.1016/j.epsc.2023.102772

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Introduction: Esophageal lung is rare bronchopulmonary foregut malformation where a main stem bronchus is connected anomalously to the esophagus. We present a challenging diagnostic workup of a 14-month-old who was referred following multiple complicated hospitalizations for recurrent respiratory distress. Case presentation: A male infant born at 37 weeks was noted to be hypoxemic at birth and subsequently diagnosed with right-sided pulmonary hypoplasia, absent right main stem bronchus, a left-sided non-obstructive pulmonary artery sling, and possible tracheal stenosis via computed tomographic angiography (CTA). After a stay in the neonatal intensive care unit for persistent hypoxemia, he was discharged home on oxygen. At 4.5 months, the patient developed severe respiratory distress requiring extracorporeal membrane oxygenation, which was complicated by a stroke. During this admission, repeat CTA showed a broncho-esophageal fistula, concerning for esophageal lung. The patient was seen in consultation at our institution at 14 months given persistent respiratory insufficiency. He underwent repeat endoscopy with our multi-disciplinary Aerodigesive Clinic, confirming mild tracheal stenosis and esophageal lung. A right pneumonectomy was recommended. During the pneumonectomy, the right bronchus was confirmed to originate from the distal esophagus on endoscopy. Intraoperative bronchoscopy showed a patent central airway and left bronchopulmonary tree. The patient recovered well post-operatively without complications and was discharged home on room air. Conclusion: Diagnosing esophageal lung can be difficult and requires thorough evaluation of the adjacent anatomy, oftentimes requiring multidisciplinary evaluation with multiple radiologic and endoscopic modalities.

引用

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