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Anasarca Revealing Severe Cardiac Involvement Due to Beh?et's Disease (BD): A Case Report
被引:0
|作者:
Smaali, Jihane
[1
,2
]
Charef, Amal
[1
]
Bamous, Mehdi
[3
]
Fatihi, Jamal
[1
]
Amezian, Taoufik
[1
]
机构:
[1] Mohammed V Mil Training Hosp, Internal Med, Rabat, Morocco
[2] Hassan II Univ, Fac Med & Pharm Casablanca, Casablanca, Morocco
[3] Mohammed V Mil Training Hosp, Cardiac Surg, Rabat, Morocco
关键词:
anasarca;
tricuspid valve regurgitation;
endomyocardial fibrosis;
intracardiac thrombosis;
beh?et?s disease;
BEHCETS-DISEASE;
D O I:
10.7759/cureus.34532
中图分类号:
R5 [内科学];
学科分类号:
1002 ;
100201 ;
摘要:
Behcet's disease (BD) is a systemic vasculitis which is most often manifested by recurrent oral aphthosis, genital aphthosis, and ocular involvement with sometimes visceral damage, in particular neurological, digestive, vascular, or renal. We report the case of a 21-year-old man admitted for anasarca who revealed severe cardiac involvement associating endomyocardial fibrosis, intracardiac thrombi and involvement of the tricuspid valve in the context of BD diagnosed a posteriori. Cardiac involvement is exceptional during BD, especially as a mode of entry into the disease. It can be particularly severe, hence the need for early diagnosis, rapid and sometimes aggressive management. Close monitoring is also necessary in order to watch for the occurrence of visceral manifestations, particularly in young patients.
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