Cronkhite-Canada Syndrome Masquerading as Inflammatory Bowel Disease

被引：1

作者：

Leong, Justin Wen Hao ^{[1
]}

Wang, Lai Mun ^{[2
]}

Li, James Weiquan ^{[1
]}

Ang, Tiing Leong ^{[1
]}

Kwek, Boon Eu Andrew ^{[1
]}

Ong, Jeannie Peng Lan ^{[1
]}

机构：

[1] Changi Gen Hosp, Dept Gastroenterol & Hepatol, Singapore, Singapore

[2] Changi Gen Hosp, Dept Lab Med, Singapore, Singapore

来源：

ACG CASE REPORTS JOURNAL | 2023年 / 10卷 / 09期

关键词：

gastrointestinal polyposis; Cronkhite-Canada syndrome; inflammatory bowel disease;

D O I：

10.14309/crj.0000000000001090

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

Cronkhite-Canada syndrome (CCS) is a rare nonhereditary gastrointestinal polyposis syndrome. We illustrate a case with clinical presentation of dysgeusia, chronic diarrhea and weight loss, and endoscopic features of diffuse gastric mucosa nodularity with circumferential nodular pancolitis and a solitary colonic polyp initially mimicking inflammatory bowel disease. After multidisciplinary discussion, the diagnosis of CCS was made. The patient received steroids with resultant clinical, endoscopic, and histological improvement. We discuss the treatment and risk of neoplasia in CCS.

引用

页数：6

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