A rare case of metastatic paraspinal rhabdomyosarcoma presenting with proptosis in an adult patient

被引:1
作者
Chanda, U. Leo [1 ]
Knapp, Christopher [2 ]
机构
[1] Univ Nottingham, Sch Med, 3 Warley Croft, Nottingham B68 9JQ, England
[2] Lincoln Cty Hosp, Dept Ophthalmol, Lincoln, England
来源
ORBIT-THE INTERNATIONAL JOURNAL ON ORBITAL DISORDERS-OCULOPLASTIC AND LACRIMAL SURGERY | 2024年 / 43卷 / 02期
关键词
Inferior rectus; metastasis; orbit; rhabdomyosarcoma; ALVEOLAR RHABDOMYOSARCOMA;
D O I
10.1080/01676830.2022.2125537
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
Secondary metastasis of rhabdomyosarcoma (RMS) to the orbit from a distant primary site is extremely rare in adults. In this article, we describe the case of a 24-year-old male presenting with proptosis, diplopia, and headaches concurrently with a histologically confirmed diagnosis of PAX3-FOXO1 positive paraspinal alveolar rhabdomyosarcoma. An orbital MRI revealed a fusiform mass arising from the inferior rectrus, displaying necrotic and irregular morphology consistent with malignancy. The patient is currently undergoing intensive chemotherapy. The objective of this case report is to highlight the rarity of an extraocular metastasis of RMS in an adult patient, alongside the importance of considering metastatic disease in a patient with fulminant unilateral proptosis.
引用
收藏
页码:280 / 282
页数:3
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