HEMOPHAGOCYTIC lymphohistiocytosis(HLH)is an aggressive and potentially fatal syndrome that results from inappropriate activation of lymphocytes and macrophages.It is characterized by fever,hepatosplenomegaly,cytopenias,hypertriglyceridemia,hypofibrinogenemia,and pathologic findings of hemophagocytosis in the bone marrow or other tissues.We report an adult HLH case admitted to hepatology department.
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Seoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South KoreaSeoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South Korea
Jung, Ji In
Kim, Ju Yeon
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Seoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South KoreaSeoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South Korea
Kim, Ju Yeon
Kim, Mi Hyeon
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Hallym Univ, Dongtan Sacred Heart Hosp, Dept Internal Med, Div Rheumatol, Hwaseong, South KoreaSeoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South Korea
Kim, Mi Hyeon
Park, Jin Kyun
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Seoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South KoreaSeoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South Korea
Park, Jin Kyun
Lee, Eun Young
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Seoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South KoreaSeoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South Korea
Lee, Eun Young
Lee, Eun Bong
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Seoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South KoreaSeoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South Korea
Lee, Eun Bong
Park, Jun Won
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Seoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South Korea
Seoul Natl Univ, Coll Med, Dept Internal Med, 101 Daehak Ro, Seoul 03080, South KoreaSeoul Natl Univ Hosp, Dept Internal Med, Div Rheumatol, Seoul, South Korea
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Natl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Juntendo Univ, Grad Sch Med, Course Adv & Specialized Med, Tokyo 1138421, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Kawamura, Yukino
Shimomura, Akihiko
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Natl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Juntendo Univ, Grad Sch Med, Course Adv & Specialized Med, Tokyo 1138421, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Shimomura, Akihiko
Taniyama, Tomoko
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Natl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Taniyama, Tomoko
Hirai, Hoshie
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Natl Ctr Global Hlth & Med, Dept Breast Surg, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Hirai, Hoshie
Hashimoto, Kazuki
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Natl Ctr Global Hlth & Med, Dept Breast Surg, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Hashimoto, Kazuki
Honda, Yayoi
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Natl Ctr Global Hlth & Med, Dept Breast Surg, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Honda, Yayoi
Kitagawa, Dai
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Natl Ctr Global Hlth & Med, Dept Breast Surg, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Kitagawa, Dai
Nasu, Ryo
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Natl Ctr Global Hlth & Med, Dept Hematol, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Nasu, Ryo
Shimazu, Hiroshi
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Natl Ctr Global Hlth & Med, Dept Hematol, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Shimazu, Hiroshi
Hangaishi, Akira
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Natl Ctr Global Hlth & Med, Dept Hematol, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
Hangaishi, Akira
Shimizu, Chikako
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Natl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, JapanNatl Ctr Global Hlth & Med, Dept Breast Med Oncol, 1-21-1 Toyama,Shinjuku Ku, Tokyo 1628655, Japan
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Unidade Local Saude Matosinhos, Internal Med Dept, Rua Dr Eduardo Torres, P-4464513 Matosinhos, PortugalUnidade Local Saude Matosinhos, Internal Med Dept, Rua Dr Eduardo Torres, P-4464513 Matosinhos, Portugal
Beires, Francisca
Laranjinha, Joana
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Hosp Pedro Hispano, Infect Dis Dept, Unidade Local Saude Matosinhos, Rua Dr Eduardo Torres, P-4464513 Matosinhos, PortugalUnidade Local Saude Matosinhos, Internal Med Dept, Rua Dr Eduardo Torres, P-4464513 Matosinhos, Portugal
Laranjinha, Joana
Pinho, Ana
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Unidade Local Saude Matosinhos, Internal Med Dept, Rua Dr Eduardo Torres, P-4464513 Matosinhos, PortugalUnidade Local Saude Matosinhos, Internal Med Dept, Rua Dr Eduardo Torres, P-4464513 Matosinhos, Portugal
Pinho, Ana
Duarte, Frederico
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Hosp Pedro Hispano, Infect Dis Dept, Unidade Local Saude Matosinhos, Rua Dr Eduardo Torres, P-4464513 Matosinhos, PortugalUnidade Local Saude Matosinhos, Internal Med Dept, Rua Dr Eduardo Torres, P-4464513 Matosinhos, Portugal