HEMOPHAGOCYTIC lymphohistiocytosis(HLH)is an aggressive and potentially fatal syndrome that results from inappropriate activation of lymphocytes and macrophages.It is characterized by fever,hepatosplenomegaly,cytopenias,hypertriglyceridemia,hypofibrinogenemia,and pathologic findings of hemophagocytosis in the bone marrow or other tissues.We report an adult HLH case admitted to hepatology department.
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Hosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, SpainHosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, Spain
Garcia-Montoya, L.
Saenz-Tenorio, C. N.
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Hosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, SpainHosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, Spain
Saenz-Tenorio, C. N.
Janta, I.
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Hosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, SpainHosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, Spain
Janta, I.
Menarguez, J.
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Hosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, SpainHosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, Spain
Menarguez, J.
Lopez-Longo, F. J.
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Hosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, SpainHosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, Spain
Lopez-Longo, F. J.
Monteagudo, I.
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Hosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, SpainHosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, Spain
Monteagudo, I.
Naredo, E.
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Hosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, SpainHosp Gen Univ Gregorio Maranon, Dept Rheumatol, 46 Dr Esquerdo, Madrid 28007, Spain
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Univ Childrens Hosp Rijeka, Div Hematol & Oncol, Rijeka 51000, CroatiaUniv Childrens Hosp Rijeka, Div Hematol & Oncol, Rijeka 51000, Croatia
Roganovic, Jelena
Kvenic, Barbara
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Univ Childrens Hosp Rijeka, Div Hematol & Oncol, Rijeka 51000, CroatiaUniv Childrens Hosp Rijeka, Div Hematol & Oncol, Rijeka 51000, Croatia
Kvenic, Barbara
Jonjic, Nives
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Univ Rijeka, Dept Pathol, Sch Med, Rijeka, CroatiaUniv Childrens Hosp Rijeka, Div Hematol & Oncol, Rijeka 51000, Croatia
Jonjic, Nives
Seili-Bekafigo, Irena
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Univ Rijeka, Dept Pathol, Sch Med, Rijeka, CroatiaUniv Childrens Hosp Rijeka, Div Hematol & Oncol, Rijeka 51000, Croatia
Seili-Bekafigo, Irena
Kardum-Skelin, Ika
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Univ Zagreb, Univ Hosp Merkur, Lab Hematol & Cytol, Zagreb, Croatia
Univ Zagreb, Sch Med, Zagreb 41001, CroatiaUniv Childrens Hosp Rijeka, Div Hematol & Oncol, Rijeka 51000, Croatia