Congenital intestinal malrotation, duodenal obstruction combined with dextrocardia: a rare case report

被引:0
作者
Yan, Jianhong [1 ]
Yang, Hang [1 ]
Xiao, Han [1 ]
Li, Chuanxin [1 ]
机构
[1] Kunming Childrens Hosp, Dept Gen Surg, Kunming, Peoples R China
关键词
intestinal malrotation; duodenal obstruction; dextrocardia; premature infant; Ladd's procedure; INFERIOR VENA-CAVA; LAPAROSCOPIC REPAIR; SITUS-INVERSUS; ANNULAR PANCREAS; VOLVULUS; INFANTS; POLYSPLENIA; ANOMALIES; CHILDREN; ABSENCE;
D O I
10.3389/fped.2025.1554891
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Background Both intestinal malrotation and situs inversus are usually asymptomatic and extremely rare. We reported a case of congenital intestinal malrotation, duodenal obstruction, dextrocardia, and pancreatic and splenic hypoplasia in a newborn. Case presentation The patient was a 17-day-old premature infant who had experienced recurrent vomiting for 5 days. Upper gastrointestinal and small intestine contrast imaging indicated intestinal malrotation and duodenal obstruction. Abdominal contrast-enhanced CT showed a small, underdeveloped pancreas, multiple nodular soft tissue densities in the area anterior to the left kidney and posterior to the stomach, and unclear splenic venous and arterial structures. Cardiac CT revealed dextrocardia with an atrial septal defect (secundum type). The laparoscopic Ladd's procedure was performed. The postoperative course was uneventful, and the patient recovered well during a 4-month follow-up. Conclusions This patient was very young and presented with multiple abnormalities. This case highlights the importance of early diagnosis, timely referral, and management of such rare congenital anomalies to achieve favorable outcomes.
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页数:6
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