A case of Sjögren's syndrome with sensory neuronopathy and polyradiculoneuropathy

被引：1

作者：

Funakoshi, Takumi ^{[1
]}

Yamada, Minoru ^{[1
]}

Ikeda, Kazuna ^{[1
]}

Yokokawa, Kazuki ^{[1
]}

Saito, Tarou ^{[1
]}

Tsuda, Reiko ^{[1
]}

Iwahara, Naotoshi ^{[1
]}

Suzuki, Syuuichirou ^{[1
]}

Hisahara, Shin ^{[1
]}

机构：

[1] Sapporo Med Univ, Sch Med, Dept Neurol, Sapporo, Japan

来源：

INTERNAL MEDICINE | 2025年

关键词：

Sj & ouml; gren syndrome; Sensory neuronopathy; Polyradiculoneuropathy; SJOGRENS-SYNDROME; PERIPHERAL NEUROPATHIES;

D O I：

10.2169/internalmedicine.5188-24

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

41-year-old female became difficulty walking due to sensory ataxia in the limbs and trunk. A diagnosis of Sj & ouml;gren's syndrome was made on the results of positive anti-SS-A antibody and a lip gland biopsy. Nerve conduction studies indicated sensory neuronopathy. The symptoms improved following treatment with plasma exchange, intravenous immunoglobulin, and intravenous methylprednisolone. Nine months later, the patient's sensory ataxia worsened. Nerve conduction studies revealed the coexistence of sensory neuronopathy and polyradiculoneuropathy. The symptoms improved following treatment with intravenous cyclophosphamide and intravenous immunoglobulin. This case represents the first instance of sensory neuronopathy and polyradiculoneuropathy coexisting as Sj & ouml;gren's syndrome related neuropathy.

引用

页数：6

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