Primary hepatic perivascular epithelioid cell tumor: A case report and review of literature

被引：1

作者：

Wannasai, Komson ^{[1
]}

Charoenchue, Puwitch ^{[2
]}

Lapisatepun, Worakitti ^{[3
]}

Wongsuriyathai, Tarathep ^{[4
]}

Kongkarnka, Sarawut ^{[1
]}

机构：

[1] Chiang Mai Univ, Fac Med, Dept Pathol, Chiang Mai 50200, Thailand

[2] Chiang Mai Univ, Fac Med, Dept Radiol, Chiang Mai 50200, Thailand

[3] Chiang Mai Univ, Fac Med, Dept Surg, Chiang Mai 50200, Thailand

[4] Chiang Mai Univ, Fac Med, Chiang Mai 50200, Thailand

来源：

HUMAN PATHOLOGY REPORTS | 2023年 / 31卷

关键词：

Primary hepatic perivascular epithelioid cell; tumor; Angiomyolipoma; Case report; PECOMA; NEOPLASM;

D O I：

10.1016/j.hpr.2023.300699

中图分类号：

R36 [病理学];

学科分类号：

100104 ;

摘要：

Primary hepatic perivascular epithelioid cell tumors (PEComas) are extremely rare soft-tissue tumors with few published reports. Herein, a case of a primary hepatic PEComa is reported, along with a review of relevant literature. A mass in the right lobe of the liver was observed during the treatment of a 24-year-old Thai woman with systemic lupus erythematosus. Imaging studies detected a liver mass in segments seven and eight. The patient underwent a right hepatectomy. A tan-brown expansile mass with well-defined borders measuring 3.5 x 4 x 3.3 cm was identified. The tumor consisted of atypical epithelioid cells arranged in a diffuse growth pattern. Thick-walled blood vessels, smooth muscle cells, myxohyaline stroma, and adipose tissue were not observed. HMB45, CD31, and actin were diffusely immunoreactive in the tumor cells, whereas CD117, S100, and hepatocyte-specific-antigen were not. Follow-up revealed recurrent hepatic tumors. This case has been described owing to the rarity of the tumor and the useful correlation between radiologic and pathological findings.

引用

页数：5

共 14 条

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