IgG4-related sclerosing cholangitis (IgG4-SC) is a unique, steroid-responsive, fibroinflammatory condition that is more commonly found in older men and is strongly associated with autoimmune pancreatitis (AIP). It may pose a diagnostic challenge at times due to closely mimicking hepatobiliary diseases such as primary sclerosing cholangitis (PSC), secondary sclerosing cholangitis (SSC), and cholangiocarcinoma. IgG4-SC has an excellent prognosis when promptly diagnosed and treated with steroids. Literature search strategy: The authors searched PubMed and Google Scholar, for articles with the search terms "autoimmune cholangiopathy" and "IgG4 cholangiopathy."
机构:
Tokyo Metropolitan Komagome Hosp, Dept Internal Med, Bunkyo Ku, Tokyo 1138677, JapanTokyo Metropolitan Komagome Hosp, Dept Internal Med, Bunkyo Ku, Tokyo 1138677, Japan
Kamisawa, Terumi
Okamoto, Atsutake
论文数: 0引用数: 0
h-index: 0
机构:
Tokyo Metropolitan Komagome Hosp, Dept Surg, Tokyo 1138677, JapanTokyo Metropolitan Komagome Hosp, Dept Internal Med, Bunkyo Ku, Tokyo 1138677, Japan
机构:
Nagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Ohara, Hirotaka
Okazaki, Kazuichi
论文数: 0引用数: 0
h-index: 0
机构:
Kansai Med Univ, Dept Internal Med 3, Hirakata, Osaka, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Okazaki, Kazuichi
Tsubouchi, Hirohito
论文数: 0引用数: 0
h-index: 0
机构:
Kagoshima Univ, Grad Sch Med & Dent Sci, Kagoshima 890, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Tsubouchi, Hirohito
Inui, Kazuo
论文数: 0引用数: 0
h-index: 0
机构:
Fujita Hlth Univ, Dept Internal Med, Teaching Hosp 2, Nagoya, Aichi, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Inui, Kazuo
Kawa, Shigeyuki
论文数: 0引用数: 0
h-index: 0
机构:
Shinshu Univ, Ctr Hlth Safety & Environm Management, Matsumoto, Nagano 390, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Kawa, Shigeyuki
Kamisawa, Terumi
论文数: 0引用数: 0
h-index: 0
机构:
Tokyo Metropolitan Komagome Hosp, Tokyo, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Kamisawa, Terumi
Tazuma, Susumu
论文数: 0引用数: 0
h-index: 0
机构:
Hiroshima Univ, Dept Gen Med, Grad Sch Med Sci, Programs Appl Med, Hiroshima, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Tazuma, Susumu
Uchida, Kazushige
论文数: 0引用数: 0
h-index: 0
机构:
Kansai Med Univ, Dept Internal Med 3, Hirakata, Osaka, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Uchida, Kazushige
论文数: 引用数:
h-index:
机构:
Hirano, Kenji
Yoshida, Hitoshi
论文数: 0引用数: 0
h-index: 0
机构:
Showa Univ, Sch Med, Div Gastroenterol, Dept Med, Tokyo 142, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Yoshida, Hitoshi
Nishino, Takayoshi
论文数: 0引用数: 0
h-index: 0
机构:
Tokyo Womens Med Univ, Dept Gastroenterol, Yachiyo Med Ctr, Tokyo, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Nishino, Takayoshi
Ko, Shigeru B. H.
论文数: 0引用数: 0
h-index: 0
机构:
Nagoya Univ, Dept Gastroenterol, Grad Sch Med, Nagoya, Aichi 4648601, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Ko, Shigeru B. H.
Mizuno, Nobumasa
论文数: 0引用数: 0
h-index: 0
机构:
Aichi Canc Ctr Hosp, Dept Gastroenterol, Nagoya, Aichi 464, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Mizuno, Nobumasa
Hamano, Hideaki
论文数: 0引用数: 0
h-index: 0
机构:
Shinshu Univ Hosp, Div Med Informat, Dept Internal Med, Matsumoto, Nagano, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Hamano, Hideaki
论文数: 引用数:
h-index:
机构:
Kanno, Atsushi
Notohara, Kenji
论文数: 0引用数: 0
h-index: 0
机构:
Kurashiki Cent Hosp, Dept Pathol, Kurashiki, Okayama, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Notohara, Kenji
Hasebe, Osamu
论文数: 0引用数: 0
h-index: 0
机构:
Nagano Municipal Hosp, Dept Gastroenterol, Nagano, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan
Hasebe, Osamu
论文数: 引用数:
h-index:
机构:
Nakazawa, Takahiro
Nakanuma, Yasuni
论文数: 0引用数: 0
h-index: 0
机构:
Kanazawa Univ, Dept Human Pathol, Grad Sch Med, Kanazawa, Ishikawa, JapanNagoya City Univ, Dept Community Based Med Educ, Grad Sch Med Sci, Mizuho Ku, Nagoya, Aichi 4678601, Japan