Cellular models of Dent disease 1 for testing the therapeutic potential of chemical chaperones

被引：0
|
作者：
Mura-Escorche, Glorian [1 ]
Ramos Trujillo, Elena [1 ]
Machado Ponce, Jose David [2 ]
Luis Yanes, Maria I. [3 ]
Claverie-Martin, Felix [1 ]
机构：
[1] Hosp Univ Nuestra Senora de Candelaria, Unidad Invest, Santa Cruz De Tenerife, Spain
[2] Univ La Laguna, Med Fis & Farmacol, Santa Cruz De Tenerife, Spain
[3] Hosp Univ Nuestra Senora de Candelaria, Serv Nefrol Pediat, Santa Cruz De Tenerife, Spain
来源：
PEDIATRIC NEPHROLOGY | 2024年 / 39卷 / 01期
关键词：
D O I：
暂无
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
162
引用
收藏
页码：S262 / S263
页数：2
相关论文
共 50 条
  • [1] The therapeutic potential of chemical chaperones in protein folding diseases
    Cortez, Leonardo
    Sim, Valerie
    PRION, 2014, 8 (02) : 197 - 202
  • [2] Chemical chaperones increase the cellular activity of N370S β-glucosidase:: A therapeutic strategy for Gaucher disease
    Sawkar, AR
    Cheng, WC
    Beutler, E
    Wong, CH
    Balch, WE
    Kelly, JW
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2002, 99 (24) : 15428 - 15433
  • [3] New Therapeutic Approaches for Krabbe Disease: The Potential of Pharmacological Chaperones
    Spratley, Samantha J.
    Deane, Janet E.
    JOURNAL OF NEUROSCIENCE RESEARCH, 2016, 94 (11) : 1203 - 1219
  • [4] Unfolding the therapeutic potential of chemical chaperones for age-related macular degeneration
    Sauer, Theodor
    Patel, Mrinali
    Chan, Chi-Chao
    Tuo, Jingsheng
    EXPERT REVIEW OF OPHTHALMOLOGY, 2008, 3 (01) : 29 - 42
  • [5] The Unfolded Protein Response-Activated Chaperone Expression in Inflammatory Bowel Disease: Exploring the Therapeutic Potential of Chemical Chaperones
    Cao, Siyan
    Kaufman, Randal J.
    GASTROENTEROLOGY, 2012, 142 (05) : S346 - S346
  • [6] Chaperones-A New Class of Potential Therapeutic Targets in Alzheimer's Disease
    Batko, Joanna
    Antosz, Katarzyna
    Miskow, Weronika
    Pszczolowska, Magdalena
    Walczak, Kamil
    Leszek, Jerzy
    INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES, 2024, 25 (06)
  • [7] ESTABLISHMENT OF CELL MODELS OF DENT'S DISEASE FOR THE DISCOVERY OF MOLECULAR TARGETS AND THERAPEUTIC SOLUTIONS
    Duran, Monica
    Sarro, Eduard
    Ariceta, Gema
    Meseguer, Anna
    NEPHROLOGY DIALYSIS TRANSPLANTATION, 2019, 34
  • [8] Gene Supplementary Therapy in Dent's Disease Mouse Models for Sustained Therapeutic Effects
    Li, Qingqi
    Yadav, Manish
    Yoo, Kyung
    Jentsch, Thomas
    Atala, Anthony
    Lu, Baisong
    MOLECULAR THERAPY, 2023, 31 (04) : 637 - 638
  • [9] PBXs: New pharmacological chaperones to increase agalactosidase A activity in Fabry disease cellular models
    Ortolano, Saida
    Pereira, Pedro Besada
    Perez, Tania
    Villar, Marta
    Moldes, Carmen Teran
    Lopez, Carlos Silva
    Pantano, Sergio
    Gomez, Ana Arevalo
    Tejado, Beatriz San Millan
    Fernandez-Martin, Julian
    MOLECULAR GENETICS AND METABOLISM, 2023, 138 (02) : 99 - 99
  • [10] The New Pharmacological Chaperones PBXs Increase α-Galactosidase A Activity in Fabry Disease Cellular Models
    Besada, Pedro
    Gallardo-Gomez, Maria
    Perez-Marquez, Tania
    Patino-alvarez, Lucia
    Pantano, Sergio
    Silva-Lopez, Carlos
    Teran, Carmen
    Arevalo-Gomez, Ana
    Ruz-Zafra, Aurora
    Fernandez-Martin, Julian
    Ortolano, Saida
    BIOMOLECULES, 2021, 11 (12)
12345