[1] Univ N Carolina, Med, Chapel Hill, NC USA
[2] Univ N Carolina, Cyst Fibrosis Pulm Res & Treatment Ctr, Chapel Hill, NC USA
[3] Univ N Carolina, Marsico Lung Inst, Chapel Hill, NC USA
[4] NHO Tokyo Natl Hosp, Ctr Pulm Dis, Kiyose, Japan
[5] Kitasato Univ, Dept Clin Med, Sch Pharm, Lab Bioregulatory Med, Minato Ku, Tokyo, Japan
[6] Univ N Carolina, Cyst Fibrosis Res Ctr, Marsico Lung Inst, Chapel Hill, NC USA
[7] UPMC, Pathol, Pittsburgh, PA USA
[8] Univ Pittsburgh, Environm & Occupat Hlth, Pittsburgh, PA USA
[9] Univ Pittsburgh, Med PACCM, Pittsburgh, PA USA