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Clinical Characteristics of Double Seropositive Myasthenia Gravis
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作者:

Lalwani, Chirag S.
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Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Movva, Hamsini
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Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Kannoth, Sudheeran
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Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham,NeuroImmunol Lab, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Nambiar, Vivek
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Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Gopinath, Siby
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Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Anandakuttan, Anandkumar
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Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Umesh, Saraf U.
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Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Narayanan, Sreelakshmi
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Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Jose, Bijoy
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Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Mathai, Annamma
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机构:
Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham,NeuroImmunol Lab, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

Leelamani, Jyothi V.
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机构:
Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham,NeuroImmunol Lab, Kochi, Kerala, India Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
机构:
[1] Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India
[2] Amrita Univ, Amrita Inst Med Sci, Dept Neurol, Amrita Vishwa Vidyapeetham,NeuroImmunol Lab, Kochi, Kerala, India
关键词:
Acetylcholine receptor antibody;
double positive myasthenia;
MuSK receptor antibody;
myasthenia gravis;
thymoma;
FREQUENCY;
ANTIBODY;
D O I:
暂无
中图分类号:
Q189 [神经科学];
学科分类号:
071006 ;
摘要:
Double seropositive myasthenia gravis (DSP-MG) has antibodies positive to both acetylcholine receptor (AChR) antibody and muscle-specific tyrosine kinase (MuSK) antibody. This study aims to delineate the clinical phenotype of DSP-MG and assess the histopathological correlation with thymoma. This is a retrospective case series conducted at a tertiary care hospital in South India between February 2018 and October 2021. We had 13 DSP-MG patients (seven females, mean age 60.77+/-14.24). The presentation was generalized in nine patients, bulbar in three, and ocular in one patient. Multi-detector computed tomography done in 11 patients showed thymoma in five and thymic hyperplasia in one. Four patients underwent thymectomy; histopathology showed Type A, B2 (n = 2), and AB thymomas. All 13 patients improved with anticholinesterases. Nine patients were administered immunosuppressants, three patients were given intravenous immunoglobulin, and a single patient underwent plasmapheresis. Our study shows that DSP-MG is more similar to the clinical phenotype of AChR-MG.
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