Behçet’s disease (BD) is an idiopathic systemic vasculitis affecting both arterial and venous vessels of all sizes, leading to a wide variety of symptoms such as recurrent oral aphthae, genital aphthae, skin lesions, ocular, neurological, vascular, articular, and gastrointestinal involvement. Ocular involvement (OI) is common in BD, affecting up to 50% of patients, generally bilaterally, and can involve both the anterior and posterior segments, posing a significant threat of vision loss. While posterior segment involvement and fundus changes in BD are common, optic disc paleness is rare. Here, we present a case of a young male with isolated optic disc paleness as the initial presentation of BD.