共 41 条
- [34] METABOLISM OF LEUCINE IN FIBROBLASTS FROM PATIENTS WITH DEFICIENCIES IN EACH OF THE MAJOR CATABOLIC ENZYMES - BRANCHED-CHAIN KETOACID DEHYDROGENASE, ISOVALERYL-COA DEHYDROGENASE, 3-METHYLCROTONYL-COA CARBOXYLASE, 3-METHYLGLUTACONYL-COA HYDRATASE, AND 3-HYDROXY-3-METHYLGLUTARYL-COA LYASE JOURNAL OF NEUROGENETICS, 1985, 2 (06) : 413 - 424