Differential diagnosis of Guillain-Barré syndrome: steroid-responsive radiculopathy in Evans syndrome

被引:0
作者
Schulten, Thomas [1 ]
Meyer, Ansgar [2 ]
Krug, Utz [3 ]
Lehmann, Helmar C. [1 ,4 ]
机构
[1] Klinikum Leverkusen, Dept Neurol, Gesundheitsprk 11, D-51375 Leverkusen, Germany
[2] Med360 Dept Radiol, Leverkusen, Germany
[3] Klinikum Leverkusen, Dept Internal Med, Leverkusen, Germany
[4] Univ Hosp Koln, Med Fac, Cologne, Germany
关键词
Guillain-Barr & eacute; syndrome; Nerve conduction; Cerebrospinal fluid; Immune thrombocytopenia; Autoimmune hemolytic anaemia;
D O I
10.1186/s42466-024-00344-1
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Guillain-Barr & eacute; syndrome is the most common acute inflammatory demyelinating peripheral nerve condition. Occasionally, other autoimmune conditions can mimic Guillain-Barr & eacute; syndrome but may require different diagnostic workup and treatment. We report here two patients with Evans syndrome, a rare hematological autoimmune condition who developed a subacute inflammatory radiculopathy. Similarities and distinguishing clinical and diagnostic features are discussed.
引用
收藏
页数:4
相关论文
共 10 条
[1]   A CASE OF AUTOIMMUNE HAEMOLYTIC ANAEMIA THROMBOCYTOPENIA AND LANDRY-GUILLAIN-BARRE SYNDROME [J].
ALA, FA ;
SHEARMAN, DJ .
ACTA HAEMATOLOGICA, 1965, 34 (06) :361-+
[2]   Evans' Syndrome: From Diagnosis to Treatment [J].
Audia, Sylvain ;
Grienay, Natacha ;
Mounier, Morgane ;
Michel, Marc ;
Bonnotte, Bernard .
JOURNAL OF CLINICAL MEDICINE, 2020, 9 (12) :1-22
[3]   Evans' syndrome: a retrospective study from the ship (French Society of Pediatric Hematology and Immunology) (36 cases) [J].
Blouin, P ;
Auvrignon, A ;
Pagnier, A ;
Thuret, I ;
Antoni, G ;
Bader-Meunier, B ;
Le Deist, F ;
Chastagner, P ;
Aladjidi, N ;
Pellier, I ;
Bertrand, Y ;
Behar, C ;
Landmann-Parker, J ;
Leverger, G ;
Perel, Y .
ARCHIVES DE PEDIATRIE, 2005, 12 (11) :1600-1607
[4]   Evans syndrome: clinical perspectives, biological insights and treatment modalities [J].
Carlos Jaime-Perez, Jose ;
Elva Aguilar-Calderon, Patrizia ;
Salazar-Cavazos, Lorena ;
Gomez-Almaguer, David .
JOURNAL OF BLOOD MEDICINE, 2018, 9 :171-184
[5]   Regional variation of Guillain-Barre syndrome [J].
Doets, Alex Y. ;
Verboon, Christine ;
van den Berg, Bianca ;
Harbo, Thomas ;
Cornblath, David R. ;
Willison, Hugh J. ;
Islam, Zhahirul ;
Attarian, Shahram ;
Barroso, Fabio A. ;
Bateman, Kathleen ;
Benedetti, Luana ;
van den Bergh, Peter ;
Casasnovas, Carlos ;
Cavaletti, Guido ;
Chavada, Govindsinh ;
Claeys, Kristl G. ;
Dardiotis, Efthimios ;
Davidson, Amy ;
van Doorn, Pieter A. ;
Feasby, Tom E. ;
Galassi, Giuliana ;
Gorson, Kenneth C. ;
Hartung, Hans-Peter ;
Hsieh, Sung-Tsang ;
Hughes, Richard A. C. ;
Illa, Isabel ;
Islam, Badrul ;
Kusunoki, Susumu ;
Kuwabara, Satoshi ;
Lehmann, Helmar C. ;
Miller, James A. L. ;
Mohammad, Quazi Deen ;
Monges, Soledad ;
Orazio, Eduardo Nobile ;
Pardo, Julio ;
Pereon, Yann ;
Rinaldi, Simon ;
Querol, Luis ;
Reddel, Stephen W. ;
Reisin, Ricardo C. ;
Shahrizaila, Nortina ;
Sindrup, Soren H. ;
Waqar, Waheed ;
Jacobs, Bart C. .
BRAIN, 2018, 141 :2866-2877
[6]  
Guez T, 1992, Eur J Med, V1, P374
[7]   Sustained remission of CIDP associated with Evans syndrome [J].
Knecht, H ;
Baumberger, M ;
Tobòn, A ;
Steck, A .
NEUROLOGY, 2004, 63 (04) :730-732
[8]   Guillain-Barre syndrome variant with prominent facial diplegia, limb paresthesia, and brisk reflexes [J].
Lehmann, Helmar C. ;
Macht, Stephan ;
Jander, Sebastian ;
Hartung, Hans-Peter ;
Methner, Axel .
JOURNAL OF NEUROLOGY, 2012, 259 (02) :370-371
[9]   Guillain-Barre-Strohl syndrome unraveled as paraneoplastic syndrome of B-cell acute lymphoblastic leukemia in a patient with preceding common variable immunodeficiency syndrome with Evans syndrome [J].
Mailänder, V ;
Gleisner, B ;
Blau, IW ;
Thiel, E .
LEUKEMIA & LYMPHOMA, 2004, 45 (01) :189-192
[10]   Guillain-Barre syndrome [J].
Shahrizaila, Nortina ;
Lehmann, Helmar C. ;
Kuwabara, Satoshi .
LANCET, 2021, 397 (10280) :1214-1228