Elevated C1s/C1-INH in serum and plasma of myasthenia gravis patients

被引:0
|
作者
Huang, Yu-Fang [1 ]
Briggs, Caitlin M. [2 ]
Gokhale, Sankalp [2 ]
Punga, Anna Rostedt [1 ]
机构
[1] Uppsala Univ, Dept Med Sci, Clin Neurophysiol, Uppsala, Sweden
[2] Dianthus Therapeut, New York, NY USA
关键词
Myasthenia gravis; Complement system; C1s; Biomarker; MOTOR END-PLATE; COMPLEMENT; COMPLEXES; LOCALIZATION; ACTIVATION; C1; C3;
D O I
10.1016/j.jneuroim.2024.578447
中图分类号
R392 [医学免疫学]; Q939.91 [免疫学];
学科分类号
100102 ;
摘要
Myasthenia Gravis (MG) is an autoimmune neuromuscular disorder where acetylcholine receptor (AChR) antibodies induce membrane attack complex formation at the muscle membrane. The C1-inhibitor (C1-INH) regulates the classical pathway and is a promising marker in other autoimmune disorders. Treatment options for AChR antibody MG include complement inhibitors; nevertheless, the early pathway activation in MG remains unclear. Serum and plasma C1s-C1-INH levels were higher in MG patients than in matched healthy controls, supporting early classical pathway activation in most MG patients. These findings allow prospective validation studies of activated C1s as a putative treatment target and potential accompanying biomarker in MG.
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页数:5
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