Pulmonary manifestations of VEXAS syndrome with acute interstitial pneumonia and diffuse alveolar hemorrhage: a case report and literature review

被引：0

作者：

Puseljic, M. ^{[1
]}

Schmid, J.

Igrec, J. ^{[1
]}

Hatzl, S. ^{[2
]}

Scholz, L. ^{[2
]}

Woelfler, A. ^{[3
]}

Fuchsjaeger, M. ^{[1
]}

Talakic, E. ^{[1
]}

机构：

[1] Med Univ Graz, Dept Radiol, Div Gen Radiol, Graz, Austria

[2] Med Univ Graz, Dept Internal Med, Intens Care Unit, Graz, Austria

[3] Med Univ Graz, Dept Internal Med, Div Hematol, Graz, Austria

来源：

ARP RHEUMATOLOGY | 2024年 / 3卷 / 02期

关键词：

Autoinflammatory disease; Interstitial lung disease; Diffuse alveolar hemorrhage; Acute interstitial; pneumonia; Computed tomography; CT FINDINGS; FEATURES;

D O I：

10.63032/EVGB1553

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome is an emerging adult-onset systemic autoinflammatory disorder affecting multiple organ systems. While lung involvement is common in this syndrome, literature regarding specific patterns is sparse. In this report, we present a case description of a patient with VEXAS syndrome who presented at the emergency department on two separate occasions with acute interstitial pneumonia (AIP) and diffuse alveolar hemorrhage (DAH). A literature review with a comparison of our observed findings to the general findings of VEXAS syndrome, AIP, and DAH is provided. This report underscores the rarity of specific pulmonary manifestations associated with VEXAS syndrome, contributing valuable insight to the limited literature available on this topic.

引用

页码：151 / 156

页数：6

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