Successful Open Repair of a Thoracoabdominal Aortic Aneurysm After Multiple Failed Endovascular Treatments in a 22-Years-Old Individual With Loeys-Dietz Syndrome

被引：0
作者：
Santoro, Annarita [1 ]
Rizk, Mohamed [1 ]
Inga Tavara, Laura [1 ]
Ramadan, Moh'd Shafiq [1 ]
Melissano, Germano [1 ]
机构：
[1] Univ Vita Salute San Raffaele, San Raffaele Sci Inst, Sch Med, Dept Vasc Surg, Via Olgettina 60, I-20132 Milan, Italy
来源：
VASCULAR AND ENDOVASCULAR SURGERY | 2025年 / 59卷 / 02期
关键词：
Loeys-Dietz syndrome; genetic aortopathies; thoracoabdominal aortic aneurysm; open aortic repair; endovascular intervention; genetically triggered disorders;
D O I：
10.1177/15385744241285112
中图分类号：
R61 [外科手术学];
学科分类号：
摘要：
Loeys-Dietz syndrome is a rare genetically triggered disease characterized by aortic involvement, predisposing individuals to aneurysm and dissection at young age. Open repair is considered the treatment of choice despite the fact that it is associated with significant morbidity and mortality rates. On the other hand, endovascular treatment may be also considered an acceptable option in specific cases such as emergency or in patients unfit for open surgery or when landing zones are within surgical grafts. We report the case of a thoracoabdominal aortic aneurysm (TAAA) open surgical repair (OSR) in a 22-year-old male patient diagnosed with type 2 Loeys-Dietz syndrome, treated by means of a TAAA replacement with a 30-mm multi-branched "Coselli" aortic graft (Vascutek, Renfrewshire, Scotland, UK) after multiple previously interventions, including a thoracic endovascular aortic repair (TEVAR) and a custom made endograft for the visceral aorta.
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页码：218 / 223
页数：6
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