Five Questions to Help Prompt End-of-Life Planning in Neuromuscular Disease

被引：1

作者：

Lipanot, Benjamin J. ^{[1
]}

Bosslet, Gabriel ^{[1
]}

机构：

[1] Indiana Univ Sch Med, Dept Med, Div Pulm Crit Care Allergy & Occupat Med, 1120 W Michigan St,CL 287, Indianapolis, IN 46202 USA

来源：

SEMINARS IN RESPIRATORY AND CRITICAL CARE MEDICINE | 2025年 / 46卷 / 03期

关键词：

neuromuscular; end of life; goals; planning; surrogates; conversation; DUCHENNE MUSCULAR-DYSTROPHY; MECHANICAL VENTILATION; DECISION-MAKING; CARE; PATIENT; TRACHEOSTOMY; INDIVIDUALS; EXPERIENCE; MANAGEMENT; PHYSICIANS;

D O I：

10.1055/s-0044-1787994

中图分类号：

R4 [临床医学];

学科分类号：

1002 ; 100602 ;

摘要：

Patients with neuromuscular disease are living longer lives but continue to have significant and often unpredictable morbidity and mortality. End-of-life planning for these patients is thus an essential part of their medical care. This planning should include the following topics: health care surrogates, swallowing and nutrition, daytime respiratory support, and all aspects of when end of life is near. Adult-onset and early-onset diseases may require different approaches to these topics. All patients with neuromuscular disease will benefit from these discussions to best reach patient-centered goals. We present health care providers these five questions and explanations as a guide.

引用

收藏

页码：233 / 239

页数：7

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