Variable Expression Common Immune Deficiency: A Report of Five Cases

被引：0
|
作者：
Bouhamdi, Abir [1 ]
Serraj, Mounia [1 ]
Biaz, Mohamed [1 ]
Benjelloun, Mohamed Chakib [1 ]
Amara, Bouchra [1 ]
机构：
[1] Univ Sidi Mohammed Ben Abdellah, Hassan Univ Hosp 2, Pulmonol Dept, Fes, Morocco
来源：
CUREUS JOURNAL OF MEDICAL SCIENCE | 2024年 / 16卷 / 05期
关键词：
systemic granulomatosis; intravenous immunoglobulins (ivig); serum protein electrophoresis (spep); bronchial dilatation; variable common immune deficiency; IMMUNODEFICIENCY DISORDERS; IMMUNOLOGICAL FEATURES; DIAGNOSTIC-CRITERIA; IMMUNOGLOBULIN;
D O I：
10.7759/cureus.61397
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
We present five cases of common variable immunodeficiency (CVID), comprising three women and two men with a mean age of 23.8 +/- 9.2 years. All our patients suffered from recurrent bronchopneumonitis, with complications of purulent pleurisy in two cases, requiring decortication in one case, and resulting in bronchiectasis in three cases. Digestive tract infections were observed in four patients, while two patients presented with ENT infections. One case was complicated by bacterial meningitis. All patients presented with global hypogammaglobulinemia, with CVID and granulomatous manifestation in one case. Treatment consisted of monthly immunoglobulin infusions.
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页数：7
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