Pediatric lymphoproliferative disorders associated with inborn errors of immunity
被引:2
|
作者:
Cheng, Jinjun
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机构:
Childrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Childrens Natl Hosp, Ctr Canc & Blood Disorders, Washington, DC USA
Childrens Natl Hosp, Ctr Canc, Washington, DC USA
Childrens Natl Hosp, Immunol Res, Washington, DC USAChildrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Cheng, Jinjun
[1
,2
,3
,4
]
Saldana, Blachy J. Davila
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h-index: 0
机构:
Childrens Natl Hosp, Ctr Canc & Blood Disorders, Washington, DC USA
Childrens Natl Hosp, Ctr Canc, Washington, DC USA
Childrens Natl Hosp, Immunol Res, Washington, DC USA
George Washington Univ, Sch Med & Hlth Sci, Washington, DC USAChildrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Saldana, Blachy J. Davila
[2
,3
,4
,5
]
Chandrakasan, Shanmuganathan
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h-index: 0
机构:
Childrens Healthcare Atlanta, Aflac Canc & Blood Disorders Ctr, Atlanta, GA USAChildrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Chandrakasan, Shanmuganathan
[6
]
Keller, Michael
论文数: 0引用数: 0
h-index: 0
机构:
Childrens Natl Hosp, Ctr Canc & Blood Disorders, Washington, DC USA
Childrens Natl Hosp, Ctr Canc, Washington, DC USA
Childrens Natl Hosp, Immunol Res, Washington, DC USAChildrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Keller, Michael
[2
,3
,4
]
机构:
[1] Childrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
[2] Childrens Natl Hosp, Ctr Canc & Blood Disorders, Washington, DC USA
[3] Childrens Natl Hosp, Ctr Canc, Washington, DC USA
[4] Childrens Natl Hosp, Immunol Res, Washington, DC USA
[5] George Washington Univ, Sch Med & Hlth Sci, Washington, DC USA
[6] Childrens Healthcare Atlanta, Aflac Canc & Blood Disorders Ctr, Atlanta, GA USA
Inborn errors of immunity;
Lymphoproliferative disorder;
Lymphoma;
EBV;
WHO classification;
International consensus classification;
CELL TRANSPLANTATION;
LYMPHOMA;
DISEASE;
MUTATIONS;
DEFICIENCY;
LUNG;
LYMPHADENOPATHY;
CLASSIFICATION;
HYPERPLASIA;
PHENOTYPE;
D O I:
10.1016/j.clim.2024.110332
中图分类号:
R392 [医学免疫学];
Q939.91 [免疫学];
学科分类号:
100102 ;
摘要:
Both non-malignant and malignant lymphoproliferative disorders (LPD) are commonly seen in patients with inborn errors of immunity (IEI), which may be the presenting manifestations or may develop during the IEI disease course. Here we review the clinical, histopathological, and molecular features of benign and malignant LPD associated with IEI and recognize the diagnostic challenges.
机构:
Univ Fed Rio de Janeiro, Fac Med, Sci Dept Brazilian Assoc Allergy & Immunol Sao Pau, Inst Puericultura & Pediat Martagao Gesteira, Sao Paulo, SP, BrazilUniv Fed Rio de Janeiro, Fac Med, Sci Dept Brazilian Assoc Allergy & Immunol Sao Pau, Inst Puericultura & Pediat Martagao Gesteira, Sao Paulo, SP, Brazil
Goudouris, Ekaterini Simoes
Felix, Mara Morelo Rocha
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h-index: 0
机构:
Univ Fed Estado Rio de Janeiro, Sch Nursing Alfredo Pinto, Internal Med & Surg, Fed Hosp State Servants,Res Dept Brazilian Assoc A, Rio de Janeiro, RJ, BrazilUniv Fed Rio de Janeiro, Fac Med, Sci Dept Brazilian Assoc Allergy & Immunol Sao Pau, Inst Puericultura & Pediat Martagao Gesteira, Sao Paulo, SP, Brazil
Felix, Mara Morelo Rocha
Kuschnir, Fabio Chigres
论文数: 0引用数: 0
h-index: 0
机构:
Univ Estadual Rio Janeiro, Fac Med Sci, President Brazilian Assoc Allergy & Immunol Sao Pa, Sao Paulo, SP, BrazilUniv Fed Rio de Janeiro, Fac Med, Sci Dept Brazilian Assoc Allergy & Immunol Sao Pau, Inst Puericultura & Pediat Martagao Gesteira, Sao Paulo, SP, Brazil
Kuschnir, Fabio Chigres
Sole, Dirceu
论文数: 0引用数: 0
h-index: 0
机构:
Univ Fed Sao Paulo, Sch Med, Res Dept Brazilian Assoc Allergy & Immunol, Sao Paulo, BrazilUniv Fed Rio de Janeiro, Fac Med, Sci Dept Brazilian Assoc Allergy & Immunol Sao Pau, Inst Puericultura & Pediat Martagao Gesteira, Sao Paulo, SP, Brazil
机构:
Tokyo Med & Dent Univ, Grad Sch Med & Dent Sci, Dept Pediat & Dev Biol, Tokyo, JapanTokyo Med & Dent Univ, Grad Sch Med & Dent Sci, Dept Pediat & Dev Biol, Tokyo, Japan
Okamoto, Keisuke
Morio, Tomohiro
论文数: 0引用数: 0
h-index: 0
机构:
Tokyo Med & Dent Univ, Grad Sch Med & Dent Sci, Dept Pediat & Dev Biol, Tokyo, JapanTokyo Med & Dent Univ, Grad Sch Med & Dent Sci, Dept Pediat & Dev Biol, Tokyo, Japan
机构:
Univ Fed Rio de Janeiro, Fac Med, Inst Puericultura & Pediat Martagao Gesteira, Sci Dept,Brazilian Assoc Allergy & Immunol, Sao Paulo, SP, BrazilUniv Fed Rio de Janeiro, Fac Med, Inst Puericultura & Pediat Martagao Gesteira, Sci Dept,Brazilian Assoc Allergy & Immunol, Sao Paulo, SP, Brazil
Goudouris, Ekaterini Simoes
Felix, Mara Morelo Rocha
论文数: 0引用数: 0
h-index: 0
机构:
Univ Fed Estado Rio de Janeiro, Fed Hosp State Servants, Sch Med & Surg, Res Dept,Brazilian Assoc Allergy & Immunol, Sao Paulo, SP, BrazilUniv Fed Rio de Janeiro, Fac Med, Inst Puericultura & Pediat Martagao Gesteira, Sci Dept,Brazilian Assoc Allergy & Immunol, Sao Paulo, SP, Brazil
Felix, Mara Morelo Rocha
Kuschnir, Fabio Chigres
论文数: 0引用数: 0
h-index: 0
机构:
Univ Estado Rio De Janeiro, Fac Med Sci, President Brazilian Assoc Allergy & Immunol, Sao Paulo, SP, BrazilUniv Fed Rio de Janeiro, Fac Med, Inst Puericultura & Pediat Martagao Gesteira, Sci Dept,Brazilian Assoc Allergy & Immunol, Sao Paulo, SP, Brazil
Kuschnir, Fabio Chigres
Sole, Dirceu
论文数: 0引用数: 0
h-index: 0
机构:
Univ Fed Sao Paulo, Sao Paulo Sch Med, Res Dept, Brazilian Assoc Allergy & Immunol, Sao Paulo, SP, BrazilUniv Fed Rio de Janeiro, Fac Med, Inst Puericultura & Pediat Martagao Gesteira, Sci Dept,Brazilian Assoc Allergy & Immunol, Sao Paulo, SP, Brazil