hamartoma;
cardio-oncology;
hamartoma of mature cardiac myocytes;
left ventricular outlet obstruction;
cardiac hamartoma;
HYPERTROPHIC CARDIOMYOPATHY;
D O I:
10.7759/cureus.62721
中图分类号:
R5 [内科学];
学科分类号:
1002 ;
100201 ;
摘要:
Hamartoma of mature cardiac myocytes (HMCM) is a rare, benign cardiac tumor. We report a case of a 19year-old female with an atypical presentation, including significant weight loss and abnormal electrocardiogram. A transthoracic echocardiogram (TTE) revealed a mass causing left ventricular outflow tract (LVOT) obstruction, confirmed by cardiac magnetic resonance (CMR) imaging showing a 5 x 3 cm mass contiguous with the right ventricular free wall and exhibiting heterogeneous, diffuse late gadolinium enhancement. The patient subsequently underwent sternotomy for surgical biopsy and septal myectomy, with histology of the mass being consistent with HMCM. The patient remained asymptomatic during her 6month follow-up.
机构:
Hosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Martinez-Vives, Pablo
Cecconi, Alberto
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h-index: 0
机构:
Hosp Univ La Princesa, Dept Cardiol, IIS IP, CIBER CV, Madrid, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Cecconi, Alberto
Vera, Alberto
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机构:
Hosp Univ Navarra, Dept Cardiol, Navarra, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Vera, Alberto
Lopez-Melgar, Beatriz
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机构:Hosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Lopez-Melgar, Beatriz
Sanz-Garcia, Ancor
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机构:Hosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Sanz-Garcia, Ancor
Viliani, Dafne
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机构:
Hosp Univ La Princesa, Dept Cardiol, IIS IP, CIBER CV, Madrid, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Viliani, Dafne
Nogales-Romo, Maria Teresa
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机构:
Hosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Nogales-Romo, Maria Teresa
Muniz, Susana Hernandez
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机构:
Hosp Univ La Princesa, Dept Radiol, Madrid, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Muniz, Susana Hernandez
Olivera, Maria Jose
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机构:
Castilla La Mancha Univ, Fac Hlth Sci, Talavera De La Reina, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Olivera, Maria Jose
Caballero, Paloma
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机构:
Hosp Univ La Princesa, Dept Radiol, Madrid, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Caballero, Paloma
Jimenez-Borreguero, Luis Jesus
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机构:
Hosp Univ La Princesa, Dept Cardiol, IIS IP, CIBER CV, Madrid, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain
Jimenez-Borreguero, Luis Jesus
Alfonso, Fernando
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机构:
Hosp Univ La Princesa, Dept Cardiol, IIS IP, CIBER CV, Madrid, SpainHosp Univ Ramon Y Cajal, Dept Cardiol, Ctra Colmenar Viejo Km 9, Madrid 28034, Spain