Navigating challenges in diagnosing acquired hemophilia A: A case report from Syria

被引:0
作者
Nayouf, Oubai [1 ]
Laflouf, Miriam [2 ]
Hamdan, Ibrahim [1 ]
Alghazawi, Ibrahim [1 ]
Aldairi, Omar [1 ]
Sulaiman, Ameen [3 ]
机构
[1] Damascus Univ, Fac Med, Damascus, Syria
[2] Damascus Univ, Fac Med, Dept Hematol, Damascus, Syria
[3] Damascus Univ, Al Mouwasat Hosp, Dept Internal Med, Hematol, Damascus, Syria
关键词
acquired hemophilia; case report; FVIII; postpartum period;
D O I
10.1002/ccr3.8811
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Acquired hemophilia A is a rare bleeding disorder. Rapid diagnosis with prolonged aPTT and low FVIII, and immediate use of bypassing agents and steroids are crucial for better outcomes, highlighting the importance of early recognition and management. Early diagnosis and intervention are crucial for better outcomes in acquired hemophilia A.image
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页数:7
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共 9 条
[1]   Acquired haemophilia A in the postpartum and risk of relapse in subsequent pregnancies: A systematic literature review [J].
Dewarrat, Natacha ;
Gavillet, Mathilde ;
Angelillo-Scherrer, Anne ;
Naveiras, Olaia ;
Grandoni, Francesco ;
Tsakiris, Dimitrios A. ;
Alberio, Lorenzo ;
Blum, Sabine .
HAEMOPHILIA, 2021, 27 (02) :199-210
[2]   Acquired Haemophilia A: A Review of What We Know [J].
Eva Mingot-Castellano, Maria ;
Javier Rodriguez-Martorell, Francisco ;
Jose Nunez-Vazquez, Ramiro ;
Marco, Pascual .
JOURNAL OF BLOOD MEDICINE, 2022, 13 :691-710
[3]   Acquired inhibitors of clotting factors: AICE recommendations for diagnosis and management [J].
Franchini, Massimo ;
Castaman, Giancarlo ;
Coppola, Antonio ;
Santoro, Cristina ;
Zanon, Ezio ;
Di Minno, Giovanni ;
Morfini, Massimo ;
Santagostino, Elena ;
Rocino, Angiola .
BLOOD TRANSFUSION, 2015, 13 (03) :498-513
[4]   Combined life-threatening internal organ bleeding and postpartum hemorrhage associated with acquired hemophilia A [J].
Kanitthamniyom, Chanakarn ;
Siladech, Pharit ;
Polpichai, Natchaya ;
Mccullough, Maireigh ;
Saowapa, Sakditad .
CLINICAL CASE REPORTS, 2024, 12 (01)
[5]   Acquired hemophilia A: Updated review of evidence and treatment guidance [J].
Kruse-Jarres, Rebecca ;
Kempton, Christine L. ;
Baudo, Francesco ;
Collins, Peter W. ;
Knoebl, Paul ;
Leissinger, Cindy A. ;
Tiede, Andreas ;
Kessler, Craig M. .
AMERICAN JOURNAL OF HEMATOLOGY, 2017, 92 (07) :695-705
[6]   Acquired Hemophilia A: Bleeding Pattern and Hemostatic Therapeutic Strategies [J].
Marino, Renato .
MEDICINA-LITHUANIA, 2023, 59 (10)
[7]   Diagnostic delay in acquired haemophilia: Analysis of causes and consequences in a 20-year Spanish cohort [J].
Pardos-Gea, J. ;
Fernandez-Diaz, N. ;
Parra, R. ;
Cortina, V. ;
Altisent, C. .
HAEMOPHILIA, 2018, 24 (03) :E163-E166
[8]   Acquired Hemophilia A: Current Guidance and Experience from Clinical Practice [J].
Pishko, Allyson M. ;
Doshi, Bhavya S. .
JOURNAL OF BLOOD MEDICINE, 2022, 13 :255-265
[9]   International recommendations on the diagnosis and treatment of acquired hemophilia A [J].
Tiede, Andreas ;
Collins, Peter ;
Knoebl, Paul ;
Teitel, Jerome ;
Kessler, Craig ;
Shima, Midori ;
Di Minno, Giovanni ;
D'Oiron, Roseline ;
Salaj, Peter ;
Jimenez-Yuste, Victor ;
Huth-Kuehne, Angela ;
Giangrande, Paul .
HAEMATOLOGICA, 2020, 105 (07) :1791-1801