The Budd-Chiari Syndrome is associated with hepatic venous outflow obstruction. This syndrome is rare in infants and children. As this syndrome is uncommon, especially in the paediatric age group, misdiagnoses and delays in the diagnosis are frequent. A high index of clinical suspicion along with a radiological aid and a histopathological correlation can lead to an early diagnosis and an appropriate management in such cases. This case report highlights the occurrence of this rare condition in the paediatric age group as well as it redefines the salient features of this syndrome.
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Zhongnan Univ, Inst Gen Surg, Changsha, Hunan, Peoples R China
Zhengzhou Univ, Dept Intervent, Henan Prov Peoples Hosp, Zhengzhou, Peoples R ChinaZhongnan Univ, Inst Gen Surg, Changsha, Hunan, Peoples R China
Liu, Shi-Yi
Xiao, Ping
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Zhongnan Univ, Inst Gen Surg, Changsha, Hunan, Peoples R ChinaZhongnan Univ, Inst Gen Surg, Changsha, Hunan, Peoples R China
Xiao, Ping
Cao, Hui-Cun
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Zhengzhou Univ, Dept Intervent, Henan Prov Peoples Hosp, Zhengzhou, Peoples R ChinaZhongnan Univ, Inst Gen Surg, Changsha, Hunan, Peoples R China
Cao, Hui-Cun
Jiang, Hao-Sheng
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Zhengzhou Univ, Dept Intervent, Henan Prov Peoples Hosp, Zhengzhou, Peoples R ChinaZhongnan Univ, Inst Gen Surg, Changsha, Hunan, Peoples R China
Jiang, Hao-Sheng
Li, Tian-Xiao
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Zhengzhou Univ, Dept Intervent, Henan Prov Peoples Hosp, Zhengzhou, Peoples R ChinaZhongnan Univ, Inst Gen Surg, Changsha, Hunan, Peoples R China
机构:
Chinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R China
Yong Liang Hosp, Dept Ultrasound, Baoding, Peoples R ChinaChinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R China
Wang, Hong-Wei
Shi, Hua-Ning
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Chengde Med Coll, Dept Ultrasound, Affiliated Hosp, Chengde, Peoples R ChinaChinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R China
Shi, Hua-Ning
Cheng, Jia
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Chinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R ChinaChinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R China
Cheng, Jia
Xie, Fang
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Chinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R ChinaChinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R China
Xie, Fang
Luo, Yu-Kun
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Chinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R ChinaChinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R China
Luo, Yu-Kun
Tang, Jie
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Chinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R ChinaChinese Peoples Liberat Army Gen Hosp, Dept Ultrasound, Beijing, Peoples R China
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Univ Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, MoroccoUniv Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, Morocco
El Hasbaoui, Brahim
Rifai, Zainab
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Univ Mohammed 5, Childrens Hosp, Fac Med & Pharm, Dept Pediat, Rabat, MoroccoUniv Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, Morocco
Rifai, Zainab
Saghir, Salahiddine
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Univ Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, MoroccoUniv Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, Morocco
Saghir, Salahiddine
Ayada, Anas
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Univ Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, MoroccoUniv Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, Morocco
Ayada, Anas
Lamalmi, Najat
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Univ Mohammed 5, Avicenne Hosp, Fac Med & Pharm, Dept Histopathol, Rabat, MoroccoUniv Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, Morocco
Lamalmi, Najat
Abilkassem, Rachid
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Univ Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, MoroccoUniv Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, Morocco
Abilkassem, Rachid
Agadr, Aomar
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Univ Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, MoroccoUniv Mohammed 5, Mil Teaching Hosp Mohammed V, Fac Med & Pharm, Dept Pediat, Rabat, Morocco