ACCUMULATION OF PIZ ALPHA-1-ANTITRYPSIN CAUSES LIVER-DAMAGE IN TRANSGENIC MICE

被引:241
作者
CARLSON, JA
ROGERS, BB
SIFERS, RN
FINEGOLD, MJ
CLIFT, SM
DEMAYO, FJ
BULLOCK, DW
WOO, SLC
机构
[1] BAYLOR COLL MED, HOWARD HUGHES MED INST, DEPT CELL BIOL, HOUSTON, TX 77030 USA
[2] BAYLOR COLL MED, HOWARD HUGHES MED INST, DEPT GASTROENTEROL, HOUSTON, TX 77030 USA
[3] BAYLOR COLL MED, HOWARD HUGHES MED INST, DEPT PATHOL, HOUSTON, TX 77030 USA
[4] BAYLOR COLL MED, INST MED GENET, HOUSTON, TX 77030 USA
关键词
D O I
10.1172/JCI113999
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1183 / 1190
页数:8
相关论文
共 24 条
  • [1] LIVER-DISEASE IN ADULTS WITH ALPHA1-ANTITRYPSIN DEFICIENCY
    BERG, NO
    ERIKSSON, S
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1972, 287 (25) : 1264 - +
  • [2] CHRONIC CRYPTOGENIC LIVER-DISEASE AND MALIGNANT HEPATOMA IN INTERMEDIATE ALPHA-1-ANTITRYPSIN DEFICIENCY IDENTIFIED BY A PI Z-SPECIFIC MONOCLONAL-ANTIBODY
    CARLSON, J
    ERIKSSON, S
    [J]. SCANDINAVIAN JOURNAL OF GASTROENTEROLOGY, 1985, 20 (07) : 835 - 842
  • [3] MULTIPLE TISSUE EXPRESS ALPHA-1-ANTITRYPSIN IN TRANSGENIC MICE AND MAN
    CARLSON, JA
    ROGERS, BB
    SIFERS, RN
    HAWKINS, HK
    FINEGOLD, MJ
    WOO, SLC
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 1988, 82 (01) : 26 - 36
  • [4] CONOVER WJ, 1980, PRACTICAL NONPARAMET, P215
  • [5] Cornelius C. E., 1988, The liver. Biology and pathobiology. Second edition., P1315
  • [6] CRUZ M, 1976, HELV PAEDIATR ACTA, V30, P501
  • [7] RISK OF CIRRHOSIS AND PRIMARY LIVER-CANCER IN ALPHA-1-ANTITRYPSIN DEFICIENCY
    ERIKSSON, S
    CARLSON, J
    VELEZ, R
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1986, 314 (12) : 736 - 739
  • [8] ERIKSSON S, 1987, ACTA MED SCAND, V221, P461
  • [9] GORDON RD, 1986, SURG CLIN N AM, V66, P541
  • [10] HETEROZYGOUS MZ ALPHA-1-ANTITRYPSIN DEFICIENCY IN ADULTS WITH CHRONIC ACTIVE HEPATITIS AND CRYPTOGENIC CIRRHOSIS
    HODGES, JR
    MILLWARDSADLER, GH
    BARBATIS, C
    WRIGHT, R
    [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1981, 304 (10) : 557 - 560