KINETIC PROPERTIES OF PARTIALLY PURIFIED PYRUVATE DEHYDROGENASE COMPLEX OF OX BRAIN

被引:51
作者
BLASS, JP
LEWIS, CA
机构
[1] UNIV CALIF, MED SCH, MENTAL RETARDATION CTR, LOS ANGELES, CA 90024 USA
[2] UNIV CALIF, MED SCH, DEPT BIOL CHEM, LOS ANGELES, CA 90024 USA
[3] UNIV CALIF, MED SCH, DEPT PSYCHIAT, LOS ANGELES, CA 90024 USA
关键词
D O I
10.1042/bj1310031
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:31 / 37
页数:7
相关论文
共 46 条
[1]  
BLASS J P, 1970, Journal of Clinical Investigation, V49, P423, DOI 10.1172/JCI106251
[2]   CLINICAL STUDIES OF A PATIENT WITH PYRUVATE DECARBOXYLASE DEFICIENCY [J].
BLASS, JP ;
KARK, RAP ;
ENGEL, WK .
ARCHIVES OF NEUROLOGY, 1971, 25 (05) :449-&
[3]   INHERITED DEFECT AFFECTING TRICARBOXYLIC ACID CYCLE IN A PATIENT WITH CONGENITAL LACTIC ACIDOSIS [J].
BLASS, JP ;
SCHULMAN, JD ;
YOUNG, DS ;
HOM, E .
JOURNAL OF CLINICAL INVESTIGATION, 1972, 51 (07) :1845-&
[4]  
BLASS JP, 1971, LANCET, V1, P1302
[5]   INHIBITION OF PYRUVATE DECARBOXYLATION IN RAT BRAIN BY ALPHA-KETOISOCAPROIC ACID [J].
BOWDEN, JA ;
MCARTHUR, CL ;
FRIED, M .
BIOCHEMICAL MEDICINE, 1971, 5 (02) :101-&
[6]   POSSIBLE BIOCHEMICAL MODEL FOR PHENYLKETONURIA [J].
BOWDEN, JA ;
MCARTHUR, CL .
NATURE, 1972, 235 (5335) :230-&
[7]   PYRUVATE DEHYDROGENASE SUBSTRATE SPECIFICITY AND PRODUCT INHIBITION [J].
BREMER, J .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1969, 8 (04) :535-&
[8]   LIPID COMPOSITION OF RAT BRAIN MYELIN AND SUBCELLULAR FRACTIONS DURING DEVELOPMENT [J].
CUZNER, ML ;
DAVISON, AN .
BIOCHEMICAL JOURNAL, 1968, 106 (01) :29-&
[9]   INSULIN ACTIVATES PYRUVATE DEHYDROGENASE IN RAT EPIDIDYMAL ADIPOSE TISSUE [J].
DENTON, RM ;
COORE, HG ;
MARTIN, BR ;
RANDLE, PJ .
NATURE-NEW BIOLOGY, 1971, 231 (21) :115-&
[10]   FURTHER OBSERVATIONS ON BIOCHEMICAL LESION IN MAPLE SYRUP URINE DISEASE [J].
DREYFUS, PM ;
PRENSKY, AL .
NATURE, 1967, 214 (5085) :276-&