STUDIES ON COMPLEMENTATION IN ARGININOSUCCINATE SYNTHETASE AND ARGININOSUCCINATE LYASE DEFICIENCIES IN HUMAN-FIBROBLASTS

被引:0
|
作者
CATHELINEAU, L
DINH, DP
BRIAND, P
KAMOUN, P
机构
关键词
D O I
暂无
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
引用
收藏
页码:282 / 284
页数:3
相关论文
共 50 条
  • [41] USE OF A CLONED CDNA TO STUDY HUMAN ARGININOSUCCINATE SYNTHETASE
    BEAUDET, AL
    SU, TS
    BOCK, HG
    EUSTACHIO, PD
    RUDDLE, FH
    OBRIEN, WE
    AMERICAN JOURNAL OF HUMAN GENETICS, 1981, 33 (06) : A36 - A36
  • [42] GENETIC-CONTROL OF ARGININOSUCCINATE SYNTHETASE IN HUMAN LYMPHOBLASTS
    IRR, JD
    JACOBY, LB
    JOURNAL OF SUPRAMOLECULAR STRUCTURE, 1977, : 74 - 74
  • [43] ARGININOSUCCINATE SYNTHETASE-ACTIVITY IN CULTURED HUMAN LYMPHOCYTES
    LOCKRIDGE, O
    SPECTOR, EB
    BLOOM, AD
    BIOCHEMICAL GENETICS, 1977, 15 (3-4) : 395 - 407
  • [44] Transient ischemia increases neuronal nitric oxide synthase, argininosuccinate synthetase and argininosuccinate lyase co-expression in rat striatal neurons
    Bizzoco, Ellsa
    Vannucchi, Maria-Giuliana
    Faussone-Pellegrini, Maria-Simonetta
    EXPERIMENTAL NEUROLOGY, 2007, 204 (01) : 252 - 259
  • [45] Coinduction of nitric oxide synthase, argininosuccinate synthetase, and argininosuccinate lyase in lipopolysaccharide-treated rats - RNA blot, immunoblot, and immunohistochemical analyses
    Nagasaki, A
    Gotoh, T
    Takeya, M
    Yu, YJ
    Takiguchi, M
    Matsuzaki, H
    Takatsuki, K
    Mori, M
    JOURNAL OF BIOLOGICAL CHEMISTRY, 1996, 271 (05) : 2658 - 2662
  • [46] HETEROGENEITY OF MUTATIONS IN ARGININOSUCCINATE SYNTHETASE CAUSING HUMAN CITRULLINEMIA
    KOBAYASHI, K
    JACKSON, MJ
    TICK, DB
    OBRIEN, WE
    BEAUDET, AL
    JOURNAL OF BIOLOGICAL CHEMISTRY, 1990, 265 (19) : 11361 - 11367
  • [47] INTERALLELIC COMPLEMENTATION IN AN INBORN ERROR OF METABOLISM - GENETIC-HETEROGENEITY IN ARGININOSUCCINATE LYASE DEFICIENCY
    MCINNES, RR
    SHIH, V
    CHILTON, S
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1984, 81 (14): : 4480 - 4484
  • [48] ARGININOSUCCINATE LYASE LEVELS IN BLOOD, LIVER AND CULTURED FIBROBLASTS OF A PATIENT WITH ARGININOSUCCINIC ACIDURIA
    POLLITT, RJ
    CLINICA CHIMICA ACTA, 1973, 46 (01) : 33 - 37
  • [49] CLONING AND SEQUENCE-ANALYSIS OF CDNA FOR HUMAN ARGININOSUCCINATE LYASE
    OBRIEN, WE
    MCINNES, R
    KALUMUCK, K
    ADCOCK, M
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1986, 83 (19) : 7211 - 7215
  • [50] ARGININOSUCCINATE LYASE - PURIFICATION AND CHARACTERIZATION FROM HUMAN-LIVER
    OBRIEN, WE
    BARR, RH
    BIOCHEMISTRY, 1981, 20 (07) : 2056 - 2060